5 major spina bifida neurosurgical issues
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Learn more about Spina Bifida at http://www.spinabifida.netTRANSCRIPT
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5 Major Spina Bifida Neurosurgical Issues
Spina Bifida Educational Resourcehttp://www.spinabifida.net
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What does “Spina Bifida” mean?
• Multiple related disorders
• Name refers to appearance on plain Xray: bifid (=split) spine
• All involve failure of the neural tube to disconnect from the skin, form a tube, and close correctly
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What does “Spina Bifida” mean?
• Some skin-covered and some not
• If not skin-covered, associated with brain malformation (Chiari II)
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Closure of Neural Tube
1. Sheet of ectoderm2. Neural “groove” forms down center3. Edges come together as a tube4. Future spinal cord breaks away from skin
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Types of Spina Bifida
• Spina bifida aperta aka”open”
• Myelomeningocele (MM)
• Most common permanently disabling birth defect in US
• Most common non-lethal CNS birth defect
• Cord non-functional at and below lesion
• Focus of today’s talk
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Spina Bifida Aperta
• Decreased incidence last 50 years
• Incidence 3.2/10,000 births
• Likely due to many factors:
• Maternal nutrition
• Folate
• Prenatal diagnosis/selective termination
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Spina Bifida Aperta Myelomeningocele
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Small Neural Placode
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Large Myelomeningocele Sac
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Intra-op View
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Don’t forget the basics!
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Any Questions?Visit http://www.spinabifida.net