referat staphylococcal scalded skin syndrome
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OLEH :
Rachma Susteriana Putri201320401011103
PEMBIMBING :
dr H! Buih "marti#i$ S%&&
RE'ER"( S("PH)LO*O**"LS*"L+E+ S&IN S)N+ROME
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PEN+"H,L,"N
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(IN-","N P,S("&"
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+E'INISI
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EPI+EMIOLOGI
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PATOFISIOLOGIToksin eksfoliatif (Ets) serin protease
Toksin berdifusi dari fokus infeksi
Tidak ada antibodi antitoksin spesifik
Proliferasi dan penyebaran di bawah barier kulit
Penyebaran toksin seara
he!ato"en ke kulit
#eni!bulkan $elah pada ikatan adhesi antar sel !olekul
des!o"lein % pada ba"ian atas epider!is (antara stratu!
spinosu! dan "ranulosu!
&ula berdindin" tipis !udah peah
'ikolsky si"n ()
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M"NI'ES("SI &LINIS
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Ga!bar 'ikolsky*s si"n positif
pada penderita SSSS
Ga!bar I!peti"o bulosa+ &ula
diisi airan keruh dan ke!udian
peah !en,adi erosi dan krusta
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Ga!bar (A) berak ke!erahan yan" !enyebar
pada len"an- !uka dan badan bayi penderita
SSSS- (&) bula berdindin" tipis yan" peah dan
!enin""alkan kesan terbakar
" B
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Ga!bar Luka yan" telah !en"erin"
dan !ulai ter,adi deskua!asi
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+I"GNOSIS
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Gam.ar : Hist/%at//i SSSS$ dimanahianna adhesi se %ada e%idermis
su%ersia
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+I"GNOSIS B"N+ING
NETNET SSSSSSSS
.sia pasien.sia pasien / tu/ tuaa / !uda/ !uda
Lesi tar"etLesi tar"et Serin" dite!ukanSerin" dite!ukan Tidak adaTidak ada
'yeri kulit 'yeri kulit 0in"an sp sedan"0in"an sp sedan" San"at nyeriSan"at nyeri
Lesi oralLesi oral .!u!nya ada.!u!nya ada 1aran"1aran"
TandaTanda Nikolsky Nikolsky () hanya di daerah lesi() hanya di daerah lesi () pada lesi 2 klt (')() pada lesi 2 klt (')
3era,at eksudasi3era,at eksudasi 4 (ta!pak der!is)4 (ta!pak der!is) % (ta!pak epder!is% (ta!pak epder!is
superfisial)superfisial)
Penye!buhanPenye!buhan / la!a/ la!a %5 6 %4 hari%5 6 %4 hari
1arin"an parut1arin"an parut Sr" dite!ukan- dpt disertaiSr" dite!ukan- dpt disertai
hiper 7 hipopi"!entasihiper 7 hipopi"!entasi1aran"1aran"
#ortalitas#ortalitas Tin""i (85 6 95 :)Tin""i (85 6 95 :) 0endah- u!u!nya se!buh0endah- u!u!nya se!buh
spontanspontan
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PENATALAKSANAAN
(u!uan (era%i untu meneradiasi in5esi S. Aureus
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MONI(ORING
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&/m%iasi dan Pr/n/sis
&/m%iasi %ain .erat an da%at ter!adi %ada%asien SSSS adaah anuan eseim.anan cairandan eetr/it&asus SSSS %ada ana !aran mene.a.an se%sis
sehina ana ematianna e.ih rendah 61789"na ematian %ada de#asa e.ih .esar 6menca%ai807;09 arena diiuti .e.era%a 5at/r %ene.a.ematian ainna dan %eninatan e!adian se%sis
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B"B 3 &ESIMP,L"N +"NPEN,(,P
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(ERIM" &"SIH
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