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Cardiac CT in Adult Congenital Heart Disease DENNIS FOLEY MEDICAL COLLEGE WISCONSIN

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Page 1: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

Cardiac CT in Adult Congenital Heart Disease

DENNIS FOLEY

MEDICAL COLLEGE WISCONSIN

Page 2: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

Adult CHD

AORTIC ANOMALIES COARCTATON , PDA

TRANSPOSITION MUSTARD

BAFFLE LEAK, STENOSIS RT VENTRICLE FAILURE

JANTENE ARTERIAL SWITCH CORONARY , PULMONARY STENOSES

TETRALOGY FALLOT POST CORRECTION PV INSUFFICIENCY

FONTAN STENOSES, PULMONARY EMBOLI CONGESTIVE HEPATOPATHY, CARDIAC CIRRHOSIS

Page 3: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

Aortic Coarctation

ISSUES DELAYED

DIAGNOSIS

POST TREATMENT SURVEILLANCE

POST TREATMENT COMPLICATIONS

Page 4: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult
Page 5: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

PSEUDO COARCTATION ASCENDING AORTIC GRAFT

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POST AORTOPLASTY

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COARCTATION ENDOSTENT

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LEFT SUBCLAVIAN FLAP AORTOPLASTY

Page 9: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

Transposition SURGICAL CORRECTION

AND COMPLICATIONS

MUSTARD/SENNING ATRIAL BAFFLE BAFFLE LEAK/

STENOSIS

RVF

JANTENE ARTERIAL SWITCH CORONARY,

PULMONARY STENOSES

Page 10: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

RV

LV

SYSTEMIC ATRIUM

PULMONARY ATRIUM

TV

RV

SYSTEMIC ATRIUM

Page 11: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

TGV , MUSTARD, PACEMAKER LEADAO

RVOT

LV

TV

SA

Page 12: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

TRANSPOSITION MUSTARD PROCEDURE

LAD

RCA

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UPPER EXT VEIN INJECTION

BAFFLE STENOSIS , LEAK

AZYGOS VEIN

IVC

Page 14: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

SECOND INJECTION DELAYED ACQUISITION

RV

AO

PA

LVLV

Page 15: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

JANTENE ARTERIAL SWITCH

PA

AS AORV

RA

LA

Page 16: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

FRONTAL

MPA

RPA

LPA

Page 17: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

TRANSPOSITION ARTERIAL SWITCH

MPA

MPA

LCARCA

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JANTENE ARTERIAL SWITCH

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Tetralogy of Fallot

INITIAL PALLIATIVE REPAIR BLALOCK TAUSSIG

WATERSTON, POTTS SHUNTS

DEFINITIVE REPAIR INFUNDIBULECTOMY

VSD CLOSURE

COMPLICATIONS PULMONARY

REGURGITATION

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PA

TETRALOGY FALLOT, INFUNDIBULECTOMY VSD REPAIR , PULMONARY VALVE INSUFFICIENCY

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CONUS BRANCH RCA

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Fontan Procedure

ATRIO PULMONARY CONNECTION

CAVO PULMONARY INTRACARDIAC ( LATERAL TUNNEL )

EXTRACARDIAC

Page 23: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

FONTAN PROCEDURE EXTRA CARDIAC CAVO PULMONARY

SIMULTANEOUS UE/IVC INJECTION

Page 24: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult
Page 25: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

NUTMEG LIVER

CARDIAC CIRRHOSIS

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CARDIAC CIRRHOSIS

REGENERATIVE NODULE

Page 27: Cardiac CT in Adult Congenital Heart Disease ·  · 2013-12-05Cardiac CT in Adult Congenital Heart Disease ... WISCONSIN. Adult CHD ... Foley - 2011 Presentation Cardiac CT in Adult

Summary

300,000 ACHD PATIENTS IN UNITED STATES

MEDICAL CARE AND SUPERVISION SPREAD BETWEEN SPECIALISED CENTERS AND PHYSICIAN PRACTICES

ROLE OF CT IMAGING THORACIC AORTA CORONARY ANOMALIES AND STENOSES STRUCTURAL ISSUES WITH PRIOR REPAIRS EXTRA CARDIAC ISSUES eg FONTAN

HEPATOPATYHY