chronic tic disorders · 7/20/16 1 chronic tic disorders what is a tic? motor simple complex...
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ChronicTicDisorders
WhatisaTic?
Motor
Simple Complex
Phonic
Simple Complex
MotorCcs
Simple-suddenbrief,meaninglessmovements– Eyeblinking,eyemovements,grimace,mouthmovements,headjerks,shouldershrugs
Complex-slower,longer,more“purposeful”– MulCplesimpleCcsoccurringinanorchestratedpaKern,facialgestures,touchingobjectsorself,handgestures,gyraCngorbending,dystonicpostures,copropraxia(obscenegestures)
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PhonicTics
Simple-suddenmeaninglesssoundsornoises– Throatclearing,coughing,sniffing,spiPng,animalnoises,grunCng,hissing,sucking,othersimplesounds
Complex-sudden,more“meaningful”u;erances– Syllables,words,phrases(“shutup”,“stopthat”)– Coprolalia(obscene,aggressivewords)– Palilalia(echoself)– Echolalia(echoothers)
OperaConalDefiniCon
• ToureKe’sDisorderA. BothmulCplemotorandoneormorevocalCcs
thathavebeenpresentatsomeCmeduringtheillness,althoughnotnecessarilyconcurrently
B. TheCcsmaywaxandwaneinfrequencybuthavepersistedformorethan1yearsincefirstCconset
C. Onsetisbeforeage18yearsD. ThedisturbanceisnotaKributabletoa
substanceorothermedicalcondiCon
OperaConalDefiniCon
• Persistent(Chronic)MotororVocalTicDisorderA. SingleormulCplemotororvocalCcsthathave
beenpresentatsomeCmeduringtheillness,butnotbothmotorandvocal
B. TheCcsmaywaxandwaneinfrequencybuthavepersistedformorethan1yearsincefirstCconset
C. Onsetisbeforeage18yearsD. ThedisturbanceisnotaKributabletoasubstance
orothermedicalcondiConE. CriteriahaveneverbeenmetforToureKe’s
disorder
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Prevalence
• ToureKe’sisaround0.77%ofchildren,0.05%ofadults
• LessseverePersistentTicDisordermaybeupto2-3%forchildren
• Manymoremalesthanfemalesdiagnosed– 2-5:1raCoseen
ToureKe’sDisorder
• Typicalageofonsetis5-6yearsold– OaenstartswithsimplefacialCcs,thenprogressestomorecomplexandmotorCcs
• Associatedwithveryhighlevelsofcomorbiddisordersandsymptoms
TicFrequency
• 97.7%SimplemotorCcs– 43.2%Eyes– 43.2%Mouth– 34.1%Facial
• 75.0%SimplevocalCcs
• 13.6%Coprolalia
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ToureKe’s&Comorbidity
• Obsessionsandcompulsions–50%
• Depression–41%
• AKenConalproblems,hyperacCvity–50-75%
• LearningdisabiliCes–51%
• PanicaKacks–13%
WhatCausesTics?
• AppearstobeanirregularityoftheneurotransmiKersdopamineandserotonin
• Thereisno“cure,”butsymptomstendtodecreaseaaeradolescenceinmostpeople
• TreatmentopConsincludedrugsandtherapy– AnCconvulsantsandneurolepCcsareusefulforsome,buthaveverynegaCvesideeffects
Can’tTheyControlIt?
• Shortanswer:No
• Controlandseveritywaxesandwanesovertheday
• Bestanalogyformostpeopleisasneeze– Youcanfeelitcomingon,canholditoffforaliKlewhile,butulCmatelyyouhavetoletitout
– Thelongermostpeopleholditin,thegreatertheseveritywhenitisletout
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HowaTicHappens
Sensory event or premonitory urge
State of inner conflict over if and when to yield to urge
Motor or Phonic Production
Transient relief sensation
ToureKe’sRelatedProblems
• Loweredoverallqualityoflife
• Academicproblems
• ImpairedsocialinteracCons
• Numberofhome-lifeimpairments– IncreasedmaritaldifficulCes,substanceabuse,familyconflict,andparenCngfrustraCon
ToureKe’sRelatedProblems
• 88%ofthosewithCcsreportanegaCveimpactontheirdailyfuncConing
• Higherunemploymentratesandloweredincomeasadults
• Self-esteemandsocialanxiety
• Physicaldamage
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CommonTriggersforTics
• Beingupsetoranxious• WatchingTV• Beingalone• Socialgatherings• Stressfullifeevents• Hearingotherscough• TalkingaboutCcs
PharmacologyforTics
• Pharmacologyisveryfrequentlyused,asfewpeoplearetrainedinbehavioraltreatments
• AnCpsychoCcsareoaenthefirstline,butusuallyfailtoeliminatetheCcsandcancause– SedaCon– Weightgain– CogniCvedulling– Tardivedyskinesiaorparkinsonism
PharmacologyforTics
• SurprisinglyfewRCTsonvariousanCpsychoCcsforCccontrol
• Clonidine(anα2adrenergicagonistandimidazolinereceptoragonist)isalsofrequentlyused,primarilyinADHD/TS
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TherapyforTics
• Gold-standardtreatmentisCogniCve-BehavioralIntervenConforTics
• Effectsizesof.7-.8foundinmeta-analyses
• Long-lasCngeffects,lowdrop-outrates,nonegaCvesideeffects
CBITOutline
• PsychoeducaCon• HabitReversalTraining• FuncConalIntervenCon• RewardSystem• RelaxaConTraining
CBITPsychoeducaCon
• PhenomenologyofCcs• PrevalenceofCcs• NaturalhistoryofCcs• Commoncomorbids• CausesofCcs• Psychosocialimpairments
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HabitReversalTraining
• Mostwell-researchedmethodtodate
• ThreecriCcalcomponents– Awarenesstraining– CompeCngresponsetraining– Socialsupport
AwarenessTraining
• InvolvesmakingclientsmoreawareofwhenandwheretheCcismostlikelytooccur
• FirststepisacompleteoperaConaldefiniConoftheCc(s)– Describewhereitoccurs,whatitlookslike,typicallocaCon(s),typicalmoodstate(s)
AwarenessTraining
• Then,anyenvironmentalfuncConsofthebehaviorneedtobeidenCfied– SociallymediatedposiCvereinforcement
• GainingaKenCon– SociallymediatednegaCvereinforcement
• EscapingfromunwantedsituaCons/acCons
– AutomaCcreinforcement• Physical/emoConalchangesthathappenfrombehavior
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AwarenessTraining
• Forhomework,clientsaretokeepanongoinglogofallCcs
• Typicallyincludesseverity,duraCon,triggers,emoCons,sensaCons,thoughts,locaCon
CompeCngResponseTraining
• Inthisphase,youteachandpracCcedoingbehaviorsthatarephysicallyincompaCblewiththeCc
• UlCmategoalistodesensiCzeclienttothe“urges”thatoaenoccur,aswellasconCnuetoraiseawareness
CompeCngResponseTraining
• CRTisverysimilartodoingEX/RPforOCD–it’sallaboutprevenConoftypicalresponsesandlePngdiscomfortnaturallydissipate
• MayneedtogethighlycreaCvetodevelopappropriatecompeCngresponses
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CompeCngResponseTraining
• Typicallybeginsbydoing“pracCce”phasewherespend30minutesadaypracCcingCcanddoingCRs
• IdenCfythemostproblemaCcCctotargetfirst
CompeCngResponsePracCce1) BasedonprioroperaConaldefiniCons,you
begintheCc
2) StarttheCc,butdonotcompleteit
3) DoCRimmediately
4) HoldtheCRfor1minuteorunClurgegoesaway,whicheverislonger
5) Rinseandrepeat
SocialSupport
• Involvesbringinglovedonesandfamilymembersintothetherapyprocessto:– ProvideposiCvefeedbackwhentheindividualengagesincompeCngresponses
– Cuethepersontoemploythesestrategies– Provideencouragementandreminderswhentheindividualisina“trigger”situaCon
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SessionBreakdownforHRT
• Session1-Interview• Session2-Awarenesstraining• Session3–CompeCngResponseTraining• Session4–CRGeneralizaCon
Session1-Interview
• FuncConalassessmentofCcs
• Assessmentofcomorbidissues
• Establishongoingassessmentplan
• Discusstreatmentoutline
YaleGlobalTicSeverity
Scale
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Session2-Awarenesstraining
• ProvideraConaleforawarenesstraining
• GetdetaileddescripConofCcs
• Discuss“warningsigns”ofCcs,establish1-3
• TherapistsimulatesCc,clienthastoacknowledgeCc
Session2-Awarenesstraining
• Repeatprocesswithwarningsigns
• Homeworkistodoself-monitoringofCcbehaviorforthenextweek
Session3–CompeCngResponseTraining
• ReviewmonitoringHW
• ChooseacompeCngresponse
• ClinicianmodelsCR
• AddressconcernsaboutCR– SituaConsitwillnotpossible,worriesaboutitfeelinguncomfortable
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Session3–CompeCngResponseTraining
• TeachclienttheCR
• Socialsupporttraining– IdenCfysupportperson– HaveclientdemonstrateCR– Havesupportpersonpraise(basedontherapistmodeling)
• HomeworkistopracCceCRfor20-30minutesdailyandconCnueself-monitoring
Session4–CRGeneralizaCon
• ReviewHW,troubleshootasneeded
• Assessself-monitoringdata
• ReviewCRtoensureit’sbeingdonecorrectly
• Asksupportpersonaboutanyproblems
Session4–CRGeneralizaCon• IntroduceuseofCRoutsideofpracCce
• Determinehowsupportperson(s)willletclientknowwhentodotheCR(iftheydon’tcatchitthemselves)
• PracCceinsession
• Homework–conCnueself-monitoringandpracCce,implementgeneralCRuse
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Sessions5+
• ReviewandtroubleshootprogressusingCRandpracCcing
• RepeatawarenessandCRprocessforotherBFRBs
• Spacesessionsouttoprovidecontactasneeded
CBITFuncCon-BasedIntervenCons
• AssessmentofantecedentsandconsequencesassociatedwithincreaseinCcs
• WorktodevelopstrategiestoreduceCcsbasedonassessment
FuncConalStrategies
• MinimizeoreliminateCcexacerbaCngsituaConswhenpossible
• RemovepotenCallyreinforcingconsequencestotheCcinCcexacerbaCngsituaCons
• WhenenteringCc-pronesituaCons,thepaCentshouldberemindedtouseHRTprocedures
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FuncConalStrategies• ForCc-pronesituaConsthatarenoteasilymodifiable,teachpaCentstrategiestominimizetheimpactofthatsituaCon– TeachingrelaxaConstrategiesforhighstresssituaCons
– TeachingcogniCverestructuring– TeachingscheduledacCvityorbreaks
• MinimizetheimpactoftheCcsonthechild– Educatepeers,teachersandrelaCvesaboutthechild’scondiCon
OCRDHomework#4
• Getintogroupsof3-4
• Decidehoweachofyouwilldoalow-tomid-levelfearexposureoverthenext3hours
• BebackattheassignedCme,readytodiscusswhatyoudidandtheresults
MediaCriCque#4