Download - Gianotti Crosti Syndrome
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Gianotti Crosti Syndrome
Elmar Johnson
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18 mánaða drengur
Um viku saga um niðurgang
Kemur nú á BMT vegna lesiona í andliti
Viku síðar eru þessi lesion orðin fleiri og ásamt því að hafa dreifst á extensor aspect framhandleggja og fótleggja.
Tilfelli
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Tilfelli (frh)
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Tilfelli (frh)
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Fyrst lýst árið 1955
Nýburar og börn
Upphaflegu greiningarskilmerkin:◦ Papular dermatitis á andliti og útlimum.◦ Paracortical hyperplasia í eitlum.◦ Akút hepatitis.
Sagan
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< 5 ára.
KK = KVK
Yfirleitt einangruð tilfelli.
Faraldrar tengdir HBV og EBV.
Faraldfræði
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HBV EBV
Aðrir pathogenar:◦ Cytomegalovirus◦ Coxsackie◦ Adenovirus◦ RS-veiran◦ HIV◦ Bólusetningar◦ O. fl o. fl o. fl…..
Orsakir
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Ónæmissvar vegna viremiu eða bacteremiu. Seinkað hypersensitivity svar.
IgE-miðlað ónæmissvar Atópískur dermatitis
Óspesifísk histopathologia◦ Vökvasöfnun í epidermis◦ Parakeratosa í efra dermis.
Pathogenesa
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Prodromal◦ Efri loftvegasýking / niðurgangspest í aðdraganda.
Önnur einkenni ◦ Slappleiki◦ Hitavella◦ Eitlastækkanir (25-35%)◦ Einkenni tengd HBV / EBV.
Klínísk mynd
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Útbrotin◦ Papular / papulovesicular ◦ Monomorphous◦ Flatur toppur◦ Bleik – brún◦ 1-10 mm í þvermál◦ Symmetría◦ Kláði (25% tilfella)
Staðsetning◦ Andlit◦ Rasskinnar◦ Extensor aspect framhandleggja og fótleggja◦ Búkur
Klínísk mynd (frh)
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Er klínísk greining◦ Útlit.◦ 3 af 4 acral svæðum affecterað.◦ ÷ Hrúður á lesionum.◦ ÷ Útbreidd og svæsin lesion á búk.
÷ Rannsóknir (nema til mismunagreiningar)◦ Húðsýni◦ Blóðprufur
Greining
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Erythema infectiosum Erythema multiforme Hand, foot and mouth disease Scabies Lichen planus
Mismunagreiningar
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GCS er selflimiting án meðferðar
10 dagar – 6 mánuðir
Horfur eru góðar og sjúkdómsgangur góðkynja.
Horfur og gangur
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Einkennameðferð◦ Kláði
Calamine lotion / andhistamín
Fræðsla◦ Orsakir◦ Horfur◦ Sjúkdómsgangur◦ Smithætta
Meðferð
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Takk fyrir!