fabrication of an auricular prosthesis in a … advance/journals/ympr/ahmad.pdf · to 67%.3-5 the...

1
FABRICATION OF AN AURICULAR PROSTHESIS IN A PATIENT WITH CONGENITAL MICROTIA: A CASE REPORT Omaid K. Ahmad DDS, MDSc, FADI , Marjorie Golden MAMS, CCA , Joseph M Huryn DDS. Maxillofacial Prosthetics, Dental Service, Department of Surgery, Memorial Sloan-Kettering Cancer Center, New York, NY. ABSTRACT This is a case report on the fabrication of an auricular prosthesis and review of literature on microtia. A five year old Asian boy presented to the Maxillofacial Prosthetics and Dental Service at the Memorial Sloan-Kettering Cancer Center. The poster discusses the step by step fabrication of the auricular prosthesis. Initial impressions of both ears were made with irreversible hydrocolloid. Left auricular wax sculpting was completed which was followed by silcone fabrication using MDX4-4210. On the next appointment tinting of the prosthesis was completed. Last appointment involved the delivery of the auricular prosthesis. REVIEW OF LITERATURE Microtia is a congenital anomaly, characterized by a small, abnormally shaped auricle (pinna). It is usually accompanied by a narrow, blocked or absent ear canal. 1, 2 The prevalence ranges from 0.83 to 17.4 per 10,000. 1,2 Microtia is more common in males, and right-sided dominance varies from 57 to 67%. 3-5 The prevalence of aural atresia or stenosis varies from 55 to 93%. 6 Epidemiological studies report that the majority of cases in China are sporadic and usually more common in males. Mothers who have prior miscarriages over 3 times or perinatal virus infection seem to be more likely to have severe microtia infants. 7 The pathogenesis of microtia is still unclear. The hereditary factors are the most probable causes since microtia is usually involved in some specific syndromes with chromosomal abnormalities, such as Goldenhar syndrome, Treacher Collins syndrome, trisomy 21 and trisomy 18. 3-5 Some maternal conditions are also considered as the risk factors of microtia, including high pregnant age , high parity , perinatal drugs using and low education. 1-3 REFERENCES 1. J. Harris, B. Kallen, E. Robert, The epidemiology of anotia and microtia, J. Med.Genet. 33 (10) (1996) 809–813. 2. E.E. Castilla, I.M. Orioli, Prevalence rates of microtia in South America, Int. J.Epidemiol. 15 (3) (1986) 364–368. 3. [P. Mastroiacovo, C. Corchia, L.D. Botto, R. Lanni, G. Zampino, D. Fusco, Epidemiology and genetics of microtia- anotia: a registry based study on over one millionbirths, J. Med. Genet. 32 (1995) 453–457 4. Llano-Rivas, A. Gonzalez-del Angel, V. Del Castillo, R. Reyes, A. Carnevale, Microtia: a clinical and genetic study at the National Institute of Pediatrics in Mexico City, Arch. Med. Res. 30 (2) (1999) 120–124. 5. G.M. Shaw, S.L. Carmichael, Z. Kaidarova, J.A. Harris, Epidemiologic characteristics of anotia and microtia in California, 1989–1997, Birth Defects Res. Clin. Mol. Teratol. 70 (2004) 472–475. 6. Klockars T, Rautio J. Embryology and epidemiology of microtia.Facial Plast Surg. 2009 Aug;25(3):145-8. Epub 2009 Oct 6. 7. Wu J, Zhang R, Zhang Q, Xu Z, Chen W, Li D.Epidemiological analysis of microtia: a retrospective study in 345 patients in China.Int J Pediatr Otorhinolaryngol. 2010 Mar;74(3):275-8. Epub 2009 Dec 29. INITIAL PHOTOGRAPHS AND IMPRESSIONS WAX SCULPTING TINTING DELIVERY

Upload: lamthu

Post on 17-Mar-2019

215 views

Category:

Documents


0 download

TRANSCRIPT

Page 1: FABRICATION OF AN AURICULAR PROSTHESIS IN A … Advance/journals/ympr/Ahmad.pdf · to 67%.3-5 The prevalence of aural atresia or stenosis varies from 55 to 93%.6 Epidemiological studies

FABRICATION OF AN AURICULAR PROSTHESIS IN A PATIENT WITH CONGENITAL MICROTIA: A CASE REPORT Omaid K. Ahmad DDS, MDSc, FADI , Marjorie Golden MAMS, CCA , Joseph M Huryn DDS.

Maxillofacial Prosthetics, Dental Service, Department of Surgery, Memorial Sloan-Kettering Cancer Center, New York, NY.

ABSTRACT This is a case report on the fabrication of an auricular prosthesis and review of literature on microtia. A five year old Asian boy presented to the Maxillofacial Prosthetics and Dental Service at the Memorial Sloan-Kettering Cancer Center.

The poster discusses the step by step fabrication of the auricular prosthesis. Initial impressions of both ears were made with irreversible hydrocolloid. Left auricular wax sculpting was completed which was followed by silcone fabrication using MDX4-4210. On the next appointment tinting of the prosthesis was completed. Last appointment involved the delivery of the auricular prosthesis.

REVIEW OF LITERATURE Microtia is a congenital anomaly, characterized by a small, abnormally shaped auricle (pinna). It is usually accompanied by a narrow, blocked or absent ear canal. 1, 2 The prevalence ranges from 0.83 to 17.4 per 10,000. 1,2 Microtia is more common in males, and right-sided dominance varies from 57 to 67%.3-5 The prevalence of aural atresia or stenosis varies from 55 to 93%.6

Epidemiological studies report that the majority of cases in China are sporadic and usually more common in males. Mothers who have prior miscarriages over 3 times or perinatal virus infection seem to be more likely to have severe microtia infants.7

The pathogenesis of microtia is still unclear. The hereditary factors are the most probable causes since microtia is usually involved in some specific syndromes with chromosomal abnormalities, such as Goldenhar syndrome, Treacher Collins syndrome, trisomy 21 and trisomy 18. 3-5Some maternal conditions are also considered as the risk factors of microtia, including high pregnant age , high parity , perinatal drugs using and low education. 1-3

 REFERENCES 1.  J. Harris, B. Kallen, E. Robert, The epidemiology of anotia and microtia, J. Med.Genet. 33 (10) (1996) 809–813. 2.  E.E. Castilla, I.M. Orioli, Prevalence rates of microtia in South America, Int. J.Epidemiol. 15 (3) (1986) 364–368. 3.  [P. Mastroiacovo, C. Corchia, L.D. Botto, R. Lanni, G. Zampino, D. Fusco, Epidemiology and genetics of microtia-

anotia: a registry based study on over one millionbirths, J. Med. Genet. 32 (1995) 453–457 4.  Llano-Rivas, A. Gonzalez-del Angel, V. Del Castillo, R. Reyes, A. Carnevale, Microtia: a clinical and genetic study at

the National Institute of Pediatrics in Mexico City, Arch. Med. Res. 30 (2) (1999) 120–124. 5.  G.M. Shaw, S.L. Carmichael, Z. Kaidarova, J.A. Harris, Epidemiologic characteristics of anotia and microtia in

California, 1989–1997, Birth Defects Res. Clin. Mol. Teratol. 70 (2004) 472–475. 6.  Klockars T, Rautio J. Embryology and epidemiology of microtia.Facial Plast Surg. 2009 Aug;25(3):145-8. Epub

2009 Oct 6. 7.  Wu J, Zhang R, Zhang Q, Xu Z, Chen W, Li D.Epidemiological analysis of microtia: a retrospective study in 345

patients in China.Int J Pediatr Otorhinolaryngol. 2010 Mar;74(3):275-8. Epub 2009 Dec 29.

INITIAL PHOTOGRAPHS AND IMPRESSIONS

WAX SCULPTING

TINTING

DELIVERY