prim haynes & franjoine 2009 child with hemiplegia margo prim haynes, pt, dpt, ma, pcs mary rose...
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Prim Haynes & Franjoine 2009
Child with Hemiplegia
Margo Prim Haynes, PT, DPT, MA, PCS
Mary Rose Franjoine, PT, DPT, MS, PCS
2009
Prim Haynes & Franjoine 2009
• Spastic or Hypertonic CP– Hemiplegia
– Diplegia
– Quadriplegia
Categories of Cerebral Palsy (CP)
Prim Haynes & Franjoine 2009
General Comments
• Hemiplegia means: Significantly more involvement on one side of the body
• Usually full term pregnancy of single births
Prim Haynes & Franjoine 2009
Pictures and Video
Prim Haynes & Franjoine 2009
General Comments
• Diagnosed early …. Why? Asymmetry Hold Bottle
Mom notices hands first
Pick up LE concerns later
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Dimension Functional Domain
Disability Domain
A. Body structure & functions
Structural & functional integrity
Impairments
A.Primary
B.Secondary
B. Motor functions Effective posture & movement
Ineffective posture & movement
C. Individual functions
Functional activities
Functional activity limitations
D. Social functions Participation Participation restriction
From: NDT Approach Theoretical Foundations & Principles of Clinical Practice, Table 2.1 pg. 82
+ Domains -
Dim
ensi
ons
NDT Enablement Classification Model of Health and Disability
Prim Haynes & Franjoine 20092009
NDT Enablement Classification Model of Health and Disability
Dimension Functional Domain Disability Domain
A. Body structure & functions
Structural & functional integrity
Impairments
A.Primary
B.Secondary
B. Motor functions Effective posture & movement
Ineffective posture & movement
C. Individual functions
Functional activities Functional activity limitations
D. Social functions Participation Participation restriction
+ Domains -
Dim
ensi
ons
From: NDT Approach Theoretical Foundations & Principles of Clinical Practice, Table 2.1 pg. 82
Prim Haynes & Franjoine 2009
• Damage (lesion) impacts- – the motor cortex – white matter projections to and from cortical
sensorimotor areas of the brain• Causes:
– Unknown prenatal condition– Asphyxia– Prematurity
• Intracranial bleeds, infection, medical conditions (Campbell S 2000)
Body Structure and Function
Prim Haynes & Franjoine 2009
CognitionFunction:
• Intelligence Varies:
– Dependent upon many factors:
– Development of seizure activity in later years (7 years)
Impairments:
– Processing
– Attention Deficit Disorders – Right vs Left Involvement (Trauner 2003)
Prim Haynes & Franjoine 2009
Neuromuscular System
Impaired Muscle Activation
• Excessive co-activation (stiffness increases) during task
– Limits movement – speed
– Limits flexibility of movement responses
Prim Haynes & Franjoine 2009
Neuromuscular System
Impaired Muscle Activation
• Impaired Muscle Synergies
– Limited repertoire
– Stereotyped patterns of movement
– Performed in limited ranges
Prim Haynes & Franjoine 2009
Neuromuscular System
Impaired Muscle Activation
• Latency in initiating
• Difficulty sustaining postural muscles
• Often passive termination of muscles
Prim Haynes & Franjoine 2009
Neuromuscular System
Impaired Motor Execution
• Impaired Modulation & Scaling of Forces
– Inability to slow down as approach target
– Particular difficulties grading grip
Prim Haynes & Franjoine 2009
Neuromuscular System
• Impaired Timing and Sequencing
• Excessive overflow of Intra-Inter limb contractions
– Decreases the capacity for isolated control during effort
Prim Haynes & Franjoine 2009
Neuromuscular System
Insufficient Force Generation (muscle strength) : Asymmetrical
• Postural Muscles
• Movement Muscles
Prim Haynes & Franjoine 2009
Sensory System
• May have:
– Hyposensitive: ↓ sensation one side
– Hypersensitive: ↑ sensitivity
– Total Disregard / Neglect
Prim Haynes & Franjoine 2009
Sensory System
• May have:
– Sensory Processing Impairment:
– Visually and auditory Impairments
Prim Haynes & Franjoine 2009
Video
Prim Haynes & Franjoine 2009
Musculoskeletal SystemSecondary Impairments
• Range of Motion Impairments: UE & LE
• Increased risk: scoliosis
• Increased risk: hip dislocation
• Monitor for limb length discrepancies both UE than LE ( UE < LE)
Prim Haynes & Franjoine 2009
NDT Enablement Classification Model of Health and Disability
Dimension Functional Domain
Disability Domain
A. Body structure & functions
Structural & functional integrity
ImpairmentsA.PrimaryB.Secondary
B. Motor functions Effective posture & movement
Ineffective posture & movement
C. Individual functions
Functional activities
Functional activity limitations
D. Social functions Participation Participation restriction
+ Domains -
Dim
ensi
ons
From: NDT Approach Theoretical Foundations & Principles of Clinical Practice, Table 2.1 pg. 82
Prim Haynes & Franjoine 2009
Posture and Movement
General Characteristics: Posture
• Underlying postural tone low
• High tone extremities, low tone trunk
• Asymmetry = poor midline orientation
Prim Haynes & Franjoine 2009
Posture and Movement
General Characteristics: Posture
• One side of the body shows more variability than the other side of body
• Uses “stronger” UE and “stronger LE to support in upright
Prim Haynes & Franjoine 2009
Posture and Movement
General Characteristics: Posture
• Difficulty transferring objects using involved hand
• Limited movement of digits / unable to get stability around wrist.
• Difficulty performing end range supination with flexion for grasp and hold
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Posture and Movement
General Characteristics: Posture
• LE patterns:
– Hip adduction, internal rotation (IR), knee flexion or extension, ankle positioned in plantar-flexion or pronated
– Hip adduction, IR, knee extension, ankle positioned in varus
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Posture and Movement
May see: Loss of independent ankle movement on involved LE
• Limited function of ant tibialis and toe extensors
• Splinting options important for this population
Prim Haynes & Franjoine 2009
Posture and Movement
General Characteristics: Movement
• Most active movement in sagittal plane
• Moves with asymmetrical phasic bursts
• Initiates movement with asymmetrical extension
Prim Haynes & Franjoine 2009
Video
Prim Haynes & Franjoine 2009
Speech and Language
• Speech and Language delays appear to resolve by school age (Trauner 2003)
• Children with LH damage more impaired in expressive language (Thal 2009, Trauner 2003)
• Children with RH damage more impaired in receptive language(Thal 2009, Trauner 2003)
• See facial asymmetry when crying, feeding and smiling- at rest see symmetry
Prim Haynes & Franjoine 2009
Prone
Postures:
• Positions on one elbow using stronger arm for play
Movement
• Pull with strong arm and push with leg to get toys
Prim Haynes & Franjoine 2009
Pictures and Video
Prim Haynes & Franjoine 2009
Supine
Postures:
• Plays in this position until move upright
Movement
• Rolls and transition from this position moving over stronger side
Prim Haynes & Franjoine 2009
Picture
Prim Haynes & Franjoine 2009
Sitting
Postures
• Sitting is a functional position
• Independent in a number of positions (“w” position, side sit, modified long sit)
• Asymmetry
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Sitting
Movement
• Often prefers to move in sitting position
– “Hitch” across floor
Prim Haynes & Franjoine 2009
Video
Prim Haynes & Franjoine 2009
Quadruped
Posture: Quadruped
• Select position when UE is strong enough to handle the movement
Movement: May see
• Asymmetrical commando crawl
• Asymmetrical reciprocal creep = pelvis behind knees
Prim Haynes & Franjoine 2009
Pictures and Video
Prim Haynes & Franjoine 2009
Kneeling
Posture
• Hips flexed, pelvis in anterior position, ankles planter flexed or dorsi flexed
• Transition to stand from kneel position
Movement
• Stabilize with upper body to move
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Standing
Postures
• Enjoy being upright
• Asymmetrical stance
Prim Haynes & Franjoine 2009
Pictures
Prim Haynes & Franjoine 2009
Walking
Movement
• Ambulation
– 80% ambulate by 2 years of age
– 100% ambulate by 3 years of age
Prim Haynes & Franjoine 2009
Video
Prim Haynes & Franjoine 2009
NDT Enablement Classification Model of Health and Disability
Dimension Functional Domain
Disability Domain
A. Body structure & functions
Structural & functional integrity
ImpairmentsA.PrimaryB.Secondary
B. Motor functions Effective posture & movement
Ineffective posture & movement
C. Individual functions
Functional activities
Functional activity limitations
D. Social functions Participation Participation restriction
+ Domains -
Dim
ensi
ons
From: NDT Approach Theoretical Foundations & Principles of Clinical Practice, Table 2.1 pg. 82
Prim Haynes & Franjoine 2009
Activities & Activities Limitation
Locomotor Skills Often independently ambulatory (3 years of age)
Communicates Communicates with /without articulation issues
Basic ADL’s May be independent with self help skills
Feeding Independent
Prim Haynes & Franjoine 2009
NDT Enablement Classification Model of Health and Disability
Dimension Functional Domain Disability Domain
A. Body structure & functions
Structural & functional integrity
Impairments
A.Primary
B.Secondary
B. Motor functions Effective posture & movement
Ineffective posture & movement
C. Individual functions
Functional activities Functional activity limitations
D. Social functions Participation Participation restriction
+ Domains -
Dim
ensi
ons
From: NDT Approach Theoretical Foundations & Principles of Clinical Practice, Table 2.1 pg. 82
Prim Haynes & Franjoine 2009
• Function well as member of family: may have difficulty keeping up with siblings
• Mainstreamed or special classroom
• May continue to higher education and full time employment
Participation
Prim Haynes & Franjoine 2009
Treatment Strategies
1. Provide somatosensory input to assist with building movement repertoire
2. Reinforce with visual and auditory clues.3. Facilitate symmetrical posture and
movement in functional tasks. Midline alignment Symmetrical strength
Prim Haynes & Franjoine 2009
Treatment Strategies
4. For hand function: choose activities that use individual finger digits (puppet play, finger tip activities)
5. Treat using rhythm and music.
Prim Haynes & Franjoine 2009
Treatment Strategies
6. Encourage child to explore world thought loading upper extremities
7. Don’t push upright position until ready to go.
8. Introduce variety and speed.
Prim Haynes & Franjoine 2009
References
• Thal DJ, Marchman, V, Stiles J, Aram D, et al. Early lexical development in children with focal brain injury. Brain Lang 2003; 40: 491-527
• Trauner D. Hemispatial neglect in young children with early unilateral brain damage. Developmental Medicine & Child Neurology 2003; 45: 160-166
Prim Haynes & Franjoine 2009
Child with Hemiplegia
Margo Prim Haynes, PT, DPT, MA, PCS
Mary Rose Franjoine, PT, DPT, MS, PCS
2009