trombopatias
DESCRIPTION
TROMBOPATIAS. DIAGNOSTICO. ANEMIA APLÁSICA. NO ESPLENOMEGALIA PANCITOPENIA MARCADA ANEMIA MARCADA NORMOCITICA NORMOCRÓMICA. EN EL F.S.P. NO HAY ERITROBLASTOS. ADE NORMAL. RETICULOCITOS AUSENTES. NEUTROPENIA SEVERA AUSENCIA DE CELULAS INMADURAS. HIPOPLASIA MEGACAROCITICA. - PowerPoint PPT PresentationTRANSCRIPT
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TROMBOPATIAS
DIAGNOSTICO
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ANEMIA APLÁSICA NO ESPLENOMEGALIA PANCITOPENIA MARCADA ANEMIA MARCADA NORMOCITICA
NORMOCRÓMICA. EN EL F.S.P. NO HAY ERITROBLASTOS. ADE NORMAL. RETICULOCITOS AUSENTES. NEUTROPENIA SEVERA AUSENCIA DE CELULAS INMADURAS
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HIPOPLASIA MEGACAROCITICA
ANEMIA DE FANCONI.SINDROME TROMBOCITOPENIA –
AUSENCIA DEL RADIO (TAR)SINDROME DE WISCOTT – ALDRICHANOMALIA DE MAY HEGGLIN
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ANOMALIA DE MAY-HEGGLIN
PLAQUETAS DE GRAN TAMAÑO (HASTA 20u).
CUERPOS DE DÖHLE.ASINTOMATICA.FUNCION PLAQUETARIA NORMAL.AUMENTO DE MEGACARIOCITOS.ULTRAESTRUCTURA ANORMAL.MADURACIÓN Y/O FRAGMENTACION
ANORMAL.
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SINDROME TAR
TROMBOCITOPENIA NEONATAL.
GRANULOS DENSOS INSUFICIENTES.
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HIPOPLASIA NEONATAL
INFECCIÓN POR RUBEOLA.EFECTO CITOTÓXICO DIRECTO
MEGACARIOCITOS DE LA MÉDULA FETAL.
MENOS DE 70000/uL.DISMINUCIÓN MARCADA O
AUSENCIA DE MEGACARIOCITOS.
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TROMBOPOYESIS INEFICAZ
ANEMIA MEGALOBLASTICAPRODUCCION PLAQUETARIA
INEFICAZ.MEGACARIOCITOS ANORMALES.PLAQUETAS GRANDES CON VIDA
MEDIA DISMINUIDA Y FUNCIÓN ANORMAL.
TROMBOCITOPENIA LEVE.
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OTRAS CAUSAS
VIRUS VIVOS (VACUNA SARAMPION) VACUOLIZACION DEGENERATIVA DE LOS MEG 6-8 DIAS DESPUES.
CITOMEGALOVIRUS. VARICELA. RUBEOLA. EPSTEIN BARR. VIRUS FIEBRE HEMORRÁGICA. MÉDULA ÓSEA INFILTRADA POR CÉLULAS
MALIGNAS.
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PTI
30-80x103/uL.PLAQUETAS MORFOLOGICAMENTE
NORMALES O GRANDES.VPM AUMENTADO.LEUCOCITOS Y ERITROCITOS
NORMALES.HIPERPLASIA MEGACARIOCITICA.
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PTI INDUCIDA POR FARMACOS
TROMBOCITOPENIA GRAVE.MENOS DE 10x103/uL.CANTIDAD DE MEGACARIOCITOS
NORMAL A ELEVADA.
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TROMBOCITOPENIA INDUCIDA POR HEPARINA.
TROMBOCITOPENIA CON TROMBOS INTRAVASCULARES.
AGREGACION PLAQUETARIA.PRUEBA DE LIBERACIÓN DE
SEROTONINA RADIOACTIVIDAD.PRUEBA DE PLAQUETAS LAVADAS INMUNOENSAYO Ac. anti-FP4.
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CID
HEMOLISIS MICROANGIOPATICA.DEPÓSITO DE TROMBOS (PLAQ+FIB).TROMBOCITOPENIA INTENSA.FACTORES V, VIII Y FIB DISMINUIDOS.DIMERO D POSITIVO.
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CRITERIOS DIAGNOSTICOS-PTT
MUJERES 30 – 40 AÑOS.HEMOLISIS.TROMBOCITOPENIA.DISFUNCIÓN NEUROLÓGICA.FIEBRE. INSUFICIENCIA RENAL PROGRESIVA.OCLUCIONES TROMBOTICAS
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DATOS DE LABORATORIO LDH Y BILIRRUBINA NO CONJUGADA
AUMENTADA. HAPTOGLOBINA BAJA. HGB MENOR A 10 g. RETICULOCITOS AUMENTADOS. ERITROCITOS NUCLEADOS. RECUENTO LEUCOCITARIO INCREMENTADO. PROTEINURIA Y HEMATURIA. HEMOGLOBINA Y HEMOSIDERINURIA. PT-PTT-TT Y FIB NORMALES. PDF Y DD AUMENTADOS.
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CRITERIOS DIAGNOSTICOS-SUH
NIÑOS PEQUEÑOS.ANEMIA HEMOLITICA
MICROANGIOPÁTICA.PLAQUETOPENIA. INSUFICIENCIA RENAL AGUDA.VEROCITOTOXINA ENDOTELIO
CAPILAR RENAL.E. COLI, SHIGELLA.
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DATOS DE LABORATORIO
ESQUISTOCITOSSUPERVIVENCIA DE PLAQUETAS
REDUCIDA.LEUCOCITOSIS MODERADA.ERITTROBLASTOSPT, PTT Y TT NORMALES.PDF AUMENTADOS.ORINA PROTEINAS Y ERITROCITOS
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AHMA CON PLAQUETOPENIA
QUIMIOTERAPIA.
ASOCIADA CON TRANSPLANTES.
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TROMBOCITOSIS
REACTIVA.ASOCIADA A HEMORRAGIA O
CIRUGIA.POSESPLENECTOMIA.ANEMIA FERROPENICA.ENFERMEDAD INFLAMATORIA.POR EJERCICIO.POR REBOTE.
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TROMBOCITOSIS
TRANSTORNOS MIELOPROLIFERATIVOS
POLICITEMIA VERA.LEUCEMIA MIELOIDE CRÓNICA.METAPLASIA MIELOIDE.TROMBOCITOPENIA ESENCIAL.
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TROMBOCITEMIA ESENCIAL
TRASTORNO MONOCLONAL. RTO PLAQUETAS MAYOR 1 MILLON/uL. POLIFERACIÓN DESCONTROLADA DE LOS
MEGACARIOCITOS EN M.O. ADULTOS Y PERSONAS MAYORES
(HOMBRES Y MUJERES). HEMORRAGIA, DISFUNCIÓN
PLAQUETARIA Y TROMBOSIS. TIEMPO DE SANGRIA NORMAL.
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TROMBOCITEMIA ESENCIAL
PLAQUETAS AGRANULARES O HIPOGRANULARES.
DE COLOR AZUL PALIDO.DE TAMAÑO HETEROGÉNEO.AGREGADOS.AGREGACIÓN AUSENTE CON
ADRENALINA, DISMINUIDA CON ADP Y NORMAL CON COLÁGENO.
ADHESIÓN DISMINUIDA.
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BERNARD - SOULIER
TIEMPO DE SANGRIA PROLONGADO. AUMENTA EL TAMAÑO DE PLAQUETAS. TROMBOCITOPENIA (50.000 – 80.000/uL). VIDA MEDIA PLAQUETARIA DISMINUIDA. 5-8u DE DIAMETRO (HASTA 20u). ME: MAYOR CANTIDAD DE VACUOLAS
CITOPLASMATICAS Y COMLPEJO DE MEMBRANA.
NO SE AGREGAN CON RISTOCETINA.
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TROMBASTENIA DE GLANZMANN
TIEMPO DE SANGRIA MUY PROLONGADO.
RECUENTO DE PLAQUETAS NORMAL.
MORFOLOGIA PLAQUETARIA NORMAL.
RETRACCIÓN DEL COÁGULO DEFICIENTE
NO AGREGACIÓN.
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SINDROME DE HERMANSKY-PUDLAK
DEFICIENCIA DE GRÁNULOS DELTA.
ASOCIADA A ALBANISMO.
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SINDROME DE CHÉDIAK-HIGASHI
CARACTERIZADO POR ALBANISMO.
DEFICIENCIA DE GRÁNULOS DELTA.
HEMORRAGIA.
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SINDROME DE WISKOT-ALDRICH
TROMBOPOYESIS INEFICAZ TROMBOCITOPENIA
DESTRUCCIÓN PLAQUETARIA
ESPECIALMENTE EN HOMBRES.PLAQUETAS PEQUEÑAS.
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SINDROME DE PLAQUETAS GRISES
AUSENCIA ESPECIFICA DE GRANULOS ALFA.
TENDENCIA DE SANGRADO LEVE.TIEMPO DE SANGRIA PROLONGADO.TROMBOCITOPENIA MODERADA.PLAQUETAS GRANDES.
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TRASTORNOS QUE AFECTAN LA FUNCIÓN
PLAQUETARIA
MIELOPROLIFERATIVOS.MIELOMA MULTIPLE.ENFERMEDAD HEPATICA.UREMIA.AFIBRINOGENEMIA.
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