cemento ossifyng fibroma of the ethmoidal cells

CEMENTO OSSIFYNG FIBROMA OF THE

ETHMOIDAL CELLSA CASE REPORT

Department of Otorhinolaryngology and Head & Neck Surgery Sestre milosrdnice hospital Zagreb

D.Shejbal, Baudoin T, Geber G, Drviš P, Stevanović S

CEMENTIFYNG FIBROMAS

• Rare benign tumors which arise from the peridontal membrane

• Multipotent cells: fibrous tissue, cementum, lammelar bones ( psammous desmo osteoblastomas)

1. Mandibula

2. Maxilla

3. Very rare in

PNS

DEVELOPMENTthree distinct stage

• I. osteolytic: cellular tissue only/ no calcified deposite

• II. Cementoblastic stage: becomes calcified and radiopaque

• III. Mature inactive stage: calcified and encapsulated ( 3,8 cm)

• Immature

• Aggressive manner

• destructive

• recidivism

PROBLEMS

• Ethmoidal location

Incoplete migration and differentiaition into peridontal membrane

( mesodermal origin)

-female, 9 years

-family history: normal, -personal history: allergy

to dermatophagoydes, pollenosis

Labaratory data, chest x ray: nornal

TWO MONTHS AGOPain in forehead, right eye,

diminished vision

ANT. RHYNOSCOPYHiperemy mucous membrane, Globe form. in middle meatus

like a conha bullosa

NMR

mucocoellae of anterior et

posterior ethmoid cells destruction lamina orbitalis

• Cemento ossifyng fybroma in the ethmoidal cells are very rare ( up to 10 cases)

• psammous desmo osteoblastomas

• Probably, this is a SECOND CASE which is a cystic lesion has performed

• Suggested craniofacial ressection/ parents refused• Micro endoscopic tumor ressection/ other hospital• Dacrocystorhinostomy• Transnasal endoscopic adenotomy• No signs of rhinoliqurrhea• Small residual tumor in the area of lamina

papyracea and no signs of dural lesion