berdon's syndrome

3
HOST 1 month old AGENT Defective gene on an autosome from Present but defective Absence of nerve cells associated No nerve impulses to rectosphincter Loss of rectosphincter Paralytic ileus Fecal Stasis Waste travel to Fecal Fecalith obstruction in Bacterial A Build up and reflux of fecal matter Intestinal B C No bowel Vomitus of green bile last 10/21/14 OGT output of Explore Laparotomy last 10/27/14 Colostomy last Signs and Symptoms: Fever Labs: 10/24/14 N.V. NEU 8.1 3 H 1.80- 8.00 WBC 14. 2 H 4.50- 13.0 MONO 2.2 6 H 0.00-. 800 BASO .28 1 H 0.00-. 200

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berdons syndrome patho

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Page 1: Berdon's Syndrome

HOST1 month oldfemale

AGENT

Defective gene on an autosome from both parents

Present but defective ganglion cells

Absence of nerve cells associated to rectosphincter

No nerve impulses to rectosphincter

Loss of rectosphincter reflex

Paralytic ileus

Fecal Stasis

Waste travel to appendix Fecal impaction

Fecalith obstruction in appendix

Bacterial growth

A

Build up and reflux of fecal matter into the stomach

Intestinal Obstruction

B C

No bowel sounds

Vomitus of green bile last 10/21/14

OGT output of greenish bilus fluid

Explore Laparotomy last 10/27/14

Colostomy last 10/27/14

Signs and Symptoms:FeverLabs:10/24/14

N.V.NEU 8.13

H1.80-8.00

WBC 14.2 H

4.50-13.0

MONO 2.26 H

0.00-.800

BASO .281 H

0.00-.200

Page 2: Berdon's Syndrome

A

Inflammation of the lumen of appendix

Appendicits

Rupture

Peritonitis

Sepsis

B C

Stool cannot be evacuated Swelling

Intestinal flora may broken down into basic components

Increase bilirubin

Signs/symptoms:-jaundiceLabsLiver Function Indirect Bilirubin result s at:10/24/14 10/28/14 11/09/14 N.V.19.23 14.30 10.23 0.10-1.00

Total Bilirubin10/24/14 10/28/14 11/09/14 N.V.19.96 16.24 15.45 0.10-1.40

Direct Bilirubin10/24/14 10/28/14 11/09/14 N.V..073 1.94 5.22 0.00-0.40

Urinalysis result last 11/15/14(+)Bilirubin

Formation of ulceration Thickening of bowel wall and narrowed intestinal passage

Obstruction causes swelling in the passage of bowel contents

Causes vomiting and abdominal distention

Signs and SymptomsWeight loss of .5kg

Abdominal distention

Appendectomy at 10/27/14

Specimen result at 10/27/14Result: Acute Appendicitis

G.I. bleeding Leakage of fecal matter

Proliferation of number of bacteria

Hemorrhagic shock due to blood loss

Sepsis

Bacteria enters the respiratory tract

Rapid fluid loss

Multiple organ failure due to inadequate circulating volume

Inflammation

Increase Vascular permeability

Inadequate perfusion

D

E

Page 3: Berdon's Syndrome

D E

Hypovolemic shock

Increase fluid accumulation in the alveoli

Signs and Symptoms:11/12/14

Nasal flaringIntercostal retractions

Use of accessory musclesLabs

Chest x-ray (11/03/14) Result:

Examination reveals there is a patch of density noted in

the left lower lung.Conclusion: Pneumonia LEFT

lower lung

Increase fluid accumulation in the alveoli

Damage ventilation

Death