berdon's syndrome
DESCRIPTION
berdons syndrome pathoTRANSCRIPT
HOST1 month oldfemale
AGENT
Defective gene on an autosome from both parents
Present but defective ganglion cells
Absence of nerve cells associated to rectosphincter
No nerve impulses to rectosphincter
Loss of rectosphincter reflex
Paralytic ileus
Fecal Stasis
Waste travel to appendix Fecal impaction
Fecalith obstruction in appendix
Bacterial growth
A
Build up and reflux of fecal matter into the stomach
Intestinal Obstruction
B C
No bowel sounds
Vomitus of green bile last 10/21/14
OGT output of greenish bilus fluid
Explore Laparotomy last 10/27/14
Colostomy last 10/27/14
Signs and Symptoms:FeverLabs:10/24/14
N.V.NEU 8.13
H1.80-8.00
WBC 14.2 H
4.50-13.0
MONO 2.26 H
0.00-.800
BASO .281 H
0.00-.200
A
Inflammation of the lumen of appendix
Appendicits
Rupture
Peritonitis
Sepsis
B C
Stool cannot be evacuated Swelling
Intestinal flora may broken down into basic components
Increase bilirubin
Signs/symptoms:-jaundiceLabsLiver Function Indirect Bilirubin result s at:10/24/14 10/28/14 11/09/14 N.V.19.23 14.30 10.23 0.10-1.00
Total Bilirubin10/24/14 10/28/14 11/09/14 N.V.19.96 16.24 15.45 0.10-1.40
Direct Bilirubin10/24/14 10/28/14 11/09/14 N.V..073 1.94 5.22 0.00-0.40
Urinalysis result last 11/15/14(+)Bilirubin
Formation of ulceration Thickening of bowel wall and narrowed intestinal passage
Obstruction causes swelling in the passage of bowel contents
Causes vomiting and abdominal distention
Signs and SymptomsWeight loss of .5kg
Abdominal distention
Appendectomy at 10/27/14
Specimen result at 10/27/14Result: Acute Appendicitis
G.I. bleeding Leakage of fecal matter
Proliferation of number of bacteria
Hemorrhagic shock due to blood loss
Sepsis
Bacteria enters the respiratory tract
Rapid fluid loss
Multiple organ failure due to inadequate circulating volume
Inflammation
Increase Vascular permeability
Inadequate perfusion
D
E
D E
Hypovolemic shock
Increase fluid accumulation in the alveoli
Signs and Symptoms:11/12/14
Nasal flaringIntercostal retractions
Use of accessory musclesLabs
Chest x-ray (11/03/14) Result:
Examination reveals there is a patch of density noted in
the left lower lung.Conclusion: Pneumonia LEFT
lower lung
Increase fluid accumulation in the alveoli
Damage ventilation
Death