female genital development - columbia university · complete vaginal duplication ... –renal...
TRANSCRIPT
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Female Genital DevelopmentFemale Genital DevelopmentRichard Schlussel M.D.
Assistant ProfessorDepartment of Urology
Columbia University
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• Normal development• Duplication• Agenesis• UG Sinus• Imperforate hymen• CAH
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Hypospadias
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Hypospadias repair
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Hypospadias repair
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• Paramesonephric duct– A.K.A. Mullerian Duct– Becomes future
• Fallopian tubes• Uterus• Upper 2/3 vagina
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VAGINAL AND UTERINEDUPLICATION
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Bicornuate Uterus
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Didelphys uterus
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Unicornuate Uterus
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Complete Vaginal Duplication
• Symptom– Blood persists despite
tampon duringmenses
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• Symptom– Upper vagina fills
with blood duringmenses
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Mayer-Rokitansky-Küster-Hauser Syndrome
1 in 5,000births
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VAGINALAGENSIS
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Normal Hymenal Ring
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Imperforate hymen
Mucous due to maternalhormones
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Intra-op drainage of imperf hymen
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UROGENITAL SINUS
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UROGENITAL SINUS
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X X
CONGENITAL ADRENAL HYPERPLASIA (CAH)
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CAH 46 XX
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• Association withUrinary TractAnomalies– Renal agenesis– Ectopic ureters