neuro pediatrica montes
TRANSCRIPT
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Alexis Montes [email protected]
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Shaken Baby Syndrome (SBS)What is it?
SBS is a medical term used to describe the injuries that can result if a baby is violently shaken.
Violent shaking is one of the most devastating forms of child abuse.
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Head movement during shaking
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Brain movement inside the skull
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Signs that a baby has been shaken
Broken bones Unusual crying Sleepiness Pale or bluish skin Vomiting or refusing to eat Not breathing Unconscious
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Tumores en pediatria
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1) Histología:
Se basa en la Clasificación de la World Health Organization en la que se consideran cuatro grupos que, para los niños, quedaría resumida en astrocitomas, meduloblastomas/tumores neuroectodérmicos primitivos (PNET), ependimomas, craneofaringiomas, tumores de células germinales y de plexos coroideos en orden decreciente de frecuencia
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2) Localización: En los niños predominan los tumores de
localización infratentorial frente a las localizaciones supratentoriales que son mayoritarias en adultos. Aproximadamente el 50% de los tumores son infratentoriales (astrocitoma cerebeloso, meduloblastoma, ependimoma y glioma de tronco); el 20% son selares o supraselares (craneofaringioma, gliomas quiasmático, talámico e hipotalámico y germinomas); y el 30% restante de localización hemisférica (astrocitomas, oligodendroglioma, PNET, ependimoma, meningioma, tumores de plexos coroideos, tumores de la región pineal y tumores de extirpe neuronal o mixta).
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3) Extensión:
Tienen más propensión a diseminarse por el espacio subaracnoideo los meduloblastomas, ependimomas y germinomas. Si la neuroimagen cerebral sugiere uno de estos tipos, es importante realizar una RNM medular con gadolinio, antes de la cirugía, así como analizar el LCR: citología, glucosa y proteínas.
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1. Síndrome de hipertensión intracraneal.
2) Signos de focalización 3) Crisis convulsivas 4) Alteraciones endocrinas 5) Coma de instauración súbita 6) Trastornos del comportamiento
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HIDROCEFALIA EN PEDIATRIA
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Causas de hidrocefalia congénita
Estenosis acueductal 33% Mielomeningocele (Arnodl Chiari) 28% Hidrocefalia comunicante 22% Malformación Dandy Walker 7% Otros 10%
J. Volpe. Neurology of the New Borne. 3a edicion, 31-35, 1994
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MMC
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