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TITLETITLE

Authors:– Affiliations, logo

Experts:– Affiliations

John Paul II Hospital in KrakówJagiellonian University, Institute of Cardiology

80 Pradnicka Str., 31-202 Krakowtel. +48 (12) 614 33 99; 614 34 88; fax. +48 (12) 614 34 88

E-mail: rarediseases@szpitaljp2.krakow.plwww.crcd.eu

DEMOGRAPHIC DATA

CASE HISTORY

CURRENT SYMTOMPS

PHYSICAL EXAMINATION

ECG

BIOCHEMICAL ANALYSIS

6-MINUTE WALK TEST

CARDIOPULMONARY EXERCISE TEST (CPX)

X-RAY

ECHOCARDIOGRAPHY

COMPUTED TOMOGRAPHY

MAGNETIC RESONANCE IMAGING

PULMONARY FUNCTION TESTS

VENTILATION/PERFUSION SCAN

HEMODYNAMIC DATA

Pressure [mmHg] REST AFTER NO INHALATION

RA

PA

RV

PCWP

LV

AORTA

Saturation [%]

VCI

VCS

RA

RV

PA

AORTA

Cardiac Output [l/min]

Cardiac Index [l/min/m2]

Qp/Qs

VPR [ARU]

TPR [ARU]

VSR [mmHg]

ANGIOGRAPHY

QUESTIONS

This slide with questions should appear many times during the presentations where

appropriate

This slide with guidelines should appear many times during the presentation after the slide with

questions where appropriate

SCIENTIFIC SOCIETIES GUIDELINES

SUGGESTED DIAGNOSTIC AND THERAPEUTIC ALGORITHM,CONCLUSIONS

John Paul II Hospital in KrakówJagiellonian University, Institute of Cardiology

80 Pradnicka Str., 31-202 Krakowtel. +48 (12) 614 33 99; 614 34 88; fax. +48 (12) 614 34 88

E-mail: rarediseases@szpitaljp2.krakow.plwww.crcd.eu

THANK YOU THANK YOU

FOR YOUR ATTENTIONFOR YOUR ATTENTION

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