thrombotic thrombocytpenic purpura_lupus_microangiopathic hemolytic anemia_plasmapheresis

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    S@G Cjsg Tbnaguugs):

    E{! I! Tbslaw Tj{elja [geer

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    J 3; r{ h`e dgij`g ~bul lgjejclg$ {jsl

    Kjcfn{hwae lbsuh{r) :224) ebjnahsge js S@G ~bul c`jss 7 @wpws agpl{bubs [gibssbha ha h{j` sug{hbes :22

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    G|jibajubha

    Chascbhws jaeChlg{gau

    _[):?5(iba

    [[);?(iba K_):3?(

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    Batgsubnjubhas Lk >!4 ni'

    U@C 45??(w` E@C A >7 @ ;3 _`u ;;???(w` [gubc ;7 '

    _KD)_h`rcl{hijsbj,d{jnigauge [KC,Splg{hcrugs

    ECU $ BCU) Agnjubtg

    C{gjubabag :!? SNHU ;3? SN_U ;7< J`f plhs :;3

    @EL 3

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    Ejujkjsg ~bul ~h{fban ebjnahsbs

    3; r{ dgij`g `wpws pjubgau Ul{hikhcruhpgabj E{hp ba lgihn`hkba (G`gtjuge [gubcs(D{jnigauge [KC Agnjubtg Chhiks

    Lgjejclg Ah{ihugasbtg Ah{ij` {gaj` dwacubha Ah{ij` _U $ J_UU

    Ibc{h Janbhpjulbc Lgih`rubc Jagibj

    & Ul{hikhcruhpgabj

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    IJLJ & Ul{hikhcruhpgabj

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    _hssbkb`bubgs ba ulbs pjubgau

    UU_ LWS EBC

    Ij`bnajau lrpg{ugasbha CJ_S LGG@_ SRAE[HIG E{wn baewcge

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    Chaebubha Jnjbasu

    LWS Ah{ij` c{gjubabag, ah dgtg{ju hasgu

    EBC Ah{ij` _U $ J_UU

    Ij`bnajaulrpg{ugasbha

    Ah{ij` K_ $ ah pjpb``gegij

    CJ_S JC@ Jk Agnjubtg

    LGG@_ Srae{hig Ahu p{gnajau

    E{wns Ah lbsuh{r

    UU_ Ahag

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    Sgb}w{gs) jaubgpb`gpubcs

    Dgtg{) jibfj (cgduj}bebig

    psgwehihajs(f`gksbg``j

    CT

    J

    I_ \ 3 _[EA : In(fn(e

    D

    wbe

    htg{h

    je

    tgaubj

    uh{

    CRC _wsg

    _`jug`gu

    @ E L

    Lk

    3 @jc

    ;3???7

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    Chw{sg $ Ijajngiga u

    Spgcbdbc U{gjuigau J`ug{ajug ejr _G 3 pw`sgs) : ni I_ _[EA):in(fn(e Crc`hplhspljibeg

    _w`sg Iw`ubp`g BT jaubkbhubcs

    Swpph{ubtg cj{g Jaub gpb`gpubcs _hujssbwi swpp`gigaujubha

    Basw`ba Iw`ubp`g _[KC DD_s js p`jsij g|cljang

    {gp`jcgigau d`wbe [E_s Igcljabcj` Tgaub`jubha

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    Dh``h~ wp

    Ju ebsclj{ng _`jug`gu chwau

    ah{ij`bsge

    Jdgk{b`g C`gj{ sgash{bwi Agpl{hubc {jang

    p{hugbaw{bj pg{sbsuban _[EA):in(fn(e Jaubgpb`gpubcs H{j` jaubkbhubcs

    _{gsgau [gcgbtge :; CRC

    kh`wsgs

    Agpl{hubc {jangp{hugbaw{bj pg{sbsuban

    J]J & @h~ ehsgsug{hbes

    JCGBs

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    _j{jebni slbdu ba UU_ Ebjnahsbs =_gauje Uh Ebje

    Ah~ HA@R ul{hikhcruhpgabj jae IJLJ ~bulhwu ja jppj{gauj`ug{ajubtg gubh`hnr j{g {gzwb{ge uh gsujk`bsl ulg ebjnahsbs jae

    babubjug p`jsij g|cljang

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    UU_ ebjnahsbs

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    JEJIUS:3 J Ebsbaugn{ba)`bfg Jae Iguj``hp{hugjsg ~bul

    Ul{hikhSphaeba urpg : {gpgjus _{hugjsg ulju c`gjtgs W@T^d Wawswj``r @j{ng Tha

    ^b``gk{jae djcuh{" ba ulg cb{cw`jubha Jksgau ba ihsu bebhpjulbc UU_ kgcjwsg hd jczwb{ge

    jwuhjaubkher balbkbuh{s", kwu ahu LWS

    JEJIUS:3 egdbcbgacr ,07'" p{gebcus=

    Bebhpjulbc UU_ Chip`gug {gsphasg uh

    p`jsij g|cljang Sw{tbtj`

    JEJIUS:3 balbkbuh{ p{gebcus=

    _{h`hange ubig uh chip`g{gsphasg

    Egjul [g`jpsg

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    C`babcj` chw{sg hd bebhpjulbc UU_ ;?' egje ~bulba ~bul 7 ~ggfs

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    UU_) S@G

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    UU_ ba S@G

    [bsf djcuh{s dh{ UU_ ba S@G) S@GEJB 1:?", agpl{bubs

    [bsf djcuh{s dh{ ba)lhspbuj` ih{uj`bur) badgcubha,

    agw{h`hnbc sripuhis Ulg ubig uh chip`gug {gibssbha ~js `hang{

    chipj{ge ~bul bebhpjulbc UU_

    Htg{j`` p{hnahsbs hd UU_ ba S@G bs phh{ Ulg ugiph hd egtg`hpigau hd UU_ ba S@G bs s`h~g{

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    Bebhpjulbc UU_ Babubj` Ulg{jprBabubjug u{gjuigau=

    _`jsij g|cljang 4? i`(fn ejb`r _`jsij badwsbha bd 1:; lhw{ eg`jr _{geabshag ; in(fn(ejr

    Chaubawg _G uh chip`gug {gsphasg=

    _`jug`gus 1:7?F(` dh{ 3 ejrs jae @EL ah{ij` jae Agw{h`hnbcj``r sujk`g

    Jdug{ chip`gug {gsphasg= _G gtg{r hulg{ ejr dh{ 5 ejrs jae suhp Ujpg{ p{geabshag [gswig u{gjuigau dh{ g|jcg{kjubha 03? ejrs"

    h{ {g`jpsg 13? ejrs"

    Ehau dh{ngu:!Ejb`r dh`bc jcbe

    ;!Jspb{ba jdug{ _`uchwau ah{ij`b}ge

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    Bebhpjulbc UU_ Sj`tjng Ulg{jpr

    [gd{jcuh{r h{ {g`jpsban ebsgjsg V:?);?' hd pjubgausY

    Bac{gjsg uh u~bcg ejb`r _`jsij G|cljang

    [buw|bijk &() crc`hplhspljibeg Tbac{bsubag Bau{jtgahws biiwag n`hkw`ba Crc`hsph{bag cja cjwsg UU_ -" Sp`gagcuhir

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    J{gjs hd Wacg{ujbaur

    Wsg hd jaub p`jug`gus jngaus ba jcwug gpbsheg Gddbcjcr hd jar ulg{jpr uh p{gtgau {g`jpsg Gddbcjcr hd _`jsij g|cljang ba sguubans `bfg phsu

    LSCU ( urpbcj` LWS(e{wn igebjuge

    Igjsw{gigau hd JEJIUS :3 jcubtbur jae busbalbkbuh{ jwuhjaubkher Kgsu d`wbe dh{ p`jsij g|cljang {gp`jcgigau d`wbe [h`g hd [buw|bijk wpd{hau j`han ~bul _G

    [gchikbajau JEJIUS :3 ulg{jpr Slhw`e jsripuhijubc pjubgaus ~bul JEJIUS:3

    egdbcbgacr kg u{gjuge8

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    Ujfg lhig igssjngs Chasbeg{ UU_ ba j`` cjsgs hd ul{hikhcruhpgabj ba S@G

    Bd UU_ h{ jurpbcj` LWS bs ha uhp hd rhw{ ebddg{gaubj` ba pu! ~bul IJLJ

    jae ul{hikhcruhpgabj, basubuwug p`jsij g|cljang js shha js phssbk`g

    Agw{h s|s j{g sgga ih{g hduga ba UU_, ~lb`g {gaj` djb`w{g bs sgga ba

    LWS

    C`jssbc(Urpbcj` LWS= ah agge dh{ p`jsij g|cljang

    JEJIUS:3 egdbcbgacr h{ balbkbuh{ bs jsshcbjuge ~bul UU_

    UU_ ba S@G ljs ih{g s`h~g{ hasgu jae j(~ phh{ {gsphasg uh [| ~bul

    bac{gjsge ih{uj`bur [buw|bijk bs j p{hibsban hpubha ba {gd{jcuh{r cjsgs

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    [bsf djcuh{s dh{ UU_

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    [bsf djcuh{s dh{ ba)lhspbuj`ih{uj`bur ba S@G pjubgaus ~bul UU_

    Chip`bcjubha Sw{tbth{s a9:5" Egjul a9:;"

    _ tj`wg

    Badgcubha :(:5 :>'" >(:; 7

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    Bacbegacg Swspgcuge UU_)LWS= :: cjsgs(ib``bha jaawj``r Bebhpjulbc UU_)LWS= 5!7 cjsgs(ib``bha jaawj``r Sgtg{g JEJIUS:3 egdbcbgacr= :!> cjsgs(ib``bha

    jaawj``r

    ) D{hi ulg Hf`jlhij UU_)LWS[gnbsu{r

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