thrombotic thrombocytpenic purpura_lupus_microangiopathic hemolytic anemia_plasmapheresis
TRANSCRIPT
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S@G Cjsg Tbnaguugs):
E{! I! Tbslaw Tj{elja [geer
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J 3; r{ h`e dgij`g ~bul lgjejclg$ {jsl
Kjcfn{hwae lbsuh{r) :224) ebjnahsge js S@G ~bul c`jss 7 @wpws agpl{bubs [gibssbha ha h{j` sug{hbes :22
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G|jibajubha
Chascbhws jaeChlg{gau
_[):?5(iba
[[);?(iba K_):3?(
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Batgsubnjubhas Lk >!4 ni'
U@C 45??(w` E@C A >7 @ ;3 _`u ;;???(w` [gubc ;7 '
_KD)_h`rcl{hijsbj,d{jnigauge [KC,Splg{hcrugs
ECU $ BCU) Agnjubtg
C{gjubabag :!? SNHU ;3? SN_U ;7< J`f plhs :;3
@EL 3
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Ejujkjsg ~bul ~h{fban ebjnahsbs
3; r{ dgij`g `wpws pjubgau Ul{hikhcruhpgabj E{hp ba lgihn`hkba (G`gtjuge [gubcs(D{jnigauge [KC Agnjubtg Chhiks
Lgjejclg Ah{ihugasbtg Ah{ij` {gaj` dwacubha Ah{ij` _U $ J_UU
Ibc{h Janbhpjulbc Lgih`rubc Jagibj
& Ul{hikhcruhpgabj
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IJLJ & Ul{hikhcruhpgabj
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_hssbkb`bubgs ba ulbs pjubgau
UU_ LWS EBC
Ij`bnajau lrpg{ugasbha CJ_S LGG@_ SRAE[HIG E{wn baewcge
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Chaebubha Jnjbasu
LWS Ah{ij` c{gjubabag, ah dgtg{ju hasgu
EBC Ah{ij` _U $ J_UU
Ij`bnajaulrpg{ugasbha
Ah{ij` K_ $ ah pjpb``gegij
CJ_S JC@ Jk Agnjubtg
LGG@_ Srae{hig Ahu p{gnajau
E{wns Ah lbsuh{r
UU_ Ahag
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Sgb}w{gs) jaubgpb`gpubcs
Dgtg{) jibfj (cgduj}bebig
psgwehihajs(f`gksbg``j
CT
J
I_ \ 3 _[EA : In(fn(e
D
wbe
htg{h
je
tgaubj
uh{
CRC _wsg
_`jug`gu
@ E L
Lk
3 @jc
;3???7
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Chw{sg $ Ijajngiga u
Spgcbdbc U{gjuigau J`ug{ajug ejr _G 3 pw`sgs) : ni I_ _[EA):in(fn(e Crc`hplhspljibeg
_w`sg Iw`ubp`g BT jaubkbhubcs
Swpph{ubtg cj{g Jaub gpb`gpubcs _hujssbwi swpp`gigaujubha
Basw`ba Iw`ubp`g _[KC DD_s js p`jsij g|cljang
{gp`jcgigau d`wbe [E_s Igcljabcj` Tgaub`jubha
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Dh``h~ wp
Ju ebsclj{ng _`jug`gu chwau
ah{ij`bsge
Jdgk{b`g C`gj{ sgash{bwi Agpl{hubc {jang
p{hugbaw{bj pg{sbsuban _[EA):in(fn(e Jaubgpb`gpubcs H{j` jaubkbhubcs
_{gsgau [gcgbtge :; CRC
kh`wsgs
Agpl{hubc {jangp{hugbaw{bj pg{sbsuban
J]J & @h~ ehsgsug{hbes
JCGBs
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_j{jebni slbdu ba UU_ Ebjnahsbs =_gauje Uh Ebje
Ah~ HA@R ul{hikhcruhpgabj jae IJLJ ~bulhwu ja jppj{gauj`ug{ajubtg gubh`hnr j{g {gzwb{ge uh gsujk`bsl ulg ebjnahsbs jae
babubjug p`jsij g|cljang
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UU_ ebjnahsbs
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JEJIUS:3 J Ebsbaugn{ba)`bfg Jae Iguj``hp{hugjsg ~bul
Ul{hikhSphaeba urpg : {gpgjus _{hugjsg ulju c`gjtgs W@T^d Wawswj``r @j{ng Tha
^b``gk{jae djcuh{" ba ulg cb{cw`jubha Jksgau ba ihsu bebhpjulbc UU_ kgcjwsg hd jczwb{ge
jwuhjaubkher balbkbuh{s", kwu ahu LWS
JEJIUS:3 egdbcbgacr ,07'" p{gebcus=
Bebhpjulbc UU_ Chip`gug {gsphasg uh
p`jsij g|cljang Sw{tbtj`
JEJIUS:3 balbkbuh{ p{gebcus=
_{h`hange ubig uh chip`g{gsphasg
Egjul [g`jpsg
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C`babcj` chw{sg hd bebhpjulbc UU_ ;?' egje ~bulba ~bul 7 ~ggfs
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UU_) S@G
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UU_ ba S@G
[bsf djcuh{s dh{ UU_ ba S@G) S@GEJB 1:?", agpl{bubs
[bsf djcuh{s dh{ ba)lhspbuj` ih{uj`bur) badgcubha,
agw{h`hnbc sripuhis Ulg ubig uh chip`gug {gibssbha ~js `hang{
chipj{ge ~bul bebhpjulbc UU_
Htg{j`` p{hnahsbs hd UU_ ba S@G bs phh{ Ulg ugiph hd egtg`hpigau hd UU_ ba S@G bs s`h~g{
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Bebhpjulbc UU_ Babubj` Ulg{jprBabubjug u{gjuigau=
_`jsij g|cljang 4? i`(fn ejb`r _`jsij badwsbha bd 1:; lhw{ eg`jr _{geabshag ; in(fn(ejr
Chaubawg _G uh chip`gug {gsphasg=
_`jug`gus 1:7?F(` dh{ 3 ejrs jae @EL ah{ij` jae Agw{h`hnbcj``r sujk`g
Jdug{ chip`gug {gsphasg= _G gtg{r hulg{ ejr dh{ 5 ejrs jae suhp Ujpg{ p{geabshag [gswig u{gjuigau dh{ g|jcg{kjubha 03? ejrs"
h{ {g`jpsg 13? ejrs"
Ehau dh{ngu:!Ejb`r dh`bc jcbe
;!Jspb{ba jdug{ _`uchwau ah{ij`b}ge
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Bebhpjulbc UU_ Sj`tjng Ulg{jpr
[gd{jcuh{r h{ {g`jpsban ebsgjsg V:?);?' hd pjubgausY
Bac{gjsg uh u~bcg ejb`r _`jsij G|cljang
[buw|bijk &() crc`hplhspljibeg Tbac{bsubag Bau{jtgahws biiwag n`hkw`ba Crc`hsph{bag cja cjwsg UU_ -" Sp`gagcuhir
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J{gjs hd Wacg{ujbaur
Wsg hd jaub p`jug`gus jngaus ba jcwug gpbsheg Gddbcjcr hd jar ulg{jpr uh p{gtgau {g`jpsg Gddbcjcr hd _`jsij g|cljang ba sguubans `bfg phsu
LSCU ( urpbcj` LWS(e{wn igebjuge
Igjsw{gigau hd JEJIUS :3 jcubtbur jae busbalbkbuh{ jwuhjaubkher Kgsu d`wbe dh{ p`jsij g|cljang {gp`jcgigau d`wbe [h`g hd [buw|bijk wpd{hau j`han ~bul _G
[gchikbajau JEJIUS :3 ulg{jpr Slhw`e jsripuhijubc pjubgaus ~bul JEJIUS:3
egdbcbgacr kg u{gjuge8
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Ujfg lhig igssjngs Chasbeg{ UU_ ba j`` cjsgs hd ul{hikhcruhpgabj ba S@G
Bd UU_ h{ jurpbcj` LWS bs ha uhp hd rhw{ ebddg{gaubj` ba pu! ~bul IJLJ
jae ul{hikhcruhpgabj, basubuwug p`jsij g|cljang js shha js phssbk`g
Agw{h s|s j{g sgga ih{g hduga ba UU_, ~lb`g {gaj` djb`w{g bs sgga ba
LWS
C`jssbc(Urpbcj` LWS= ah agge dh{ p`jsij g|cljang
JEJIUS:3 egdbcbgacr h{ balbkbuh{ bs jsshcbjuge ~bul UU_
UU_ ba S@G ljs ih{g s`h~g{ hasgu jae j(~ phh{ {gsphasg uh [| ~bul
bac{gjsge ih{uj`bur [buw|bijk bs j p{hibsban hpubha ba {gd{jcuh{r cjsgs
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[bsf djcuh{s dh{ UU_
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[bsf djcuh{s dh{ ba)lhspbuj`ih{uj`bur ba S@G pjubgaus ~bul UU_
Chip`bcjubha Sw{tbth{s a9:5" Egjul a9:;"
_ tj`wg
Badgcubha :(:5 :>'" >(:; 7
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Bacbegacg Swspgcuge UU_)LWS= :: cjsgs(ib``bha jaawj``r Bebhpjulbc UU_)LWS= 5!7 cjsgs(ib``bha jaawj``r Sgtg{g JEJIUS:3 egdbcbgacr= :!> cjsgs(ib``bha
jaawj``r
) D{hi ulg Hf`jlhij UU_)LWS[gnbsu{r
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