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STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA Major Birth Defects Data from Population-based Birth Defects Surveillance Programs in the United States, 2012-2016 The introduction, data collection procedure, and birth defects codes for the state-specific birth defects data are available in the article, “Population-based birth defects data in the United States, 2012-2016: A focus on abdominal wall defects.” Additional information and program contacts on population-based birth defects surveillance programs are available on page S126-S180. The state-specific birth defects tables were prepared by the National Center on Birth Defects and Developmental Disabilities, Centers for Disease Control and Prevention and approved by the state programs in September 2019. The 42 population-based birth defects programs contributing data include: Alaska Birth Defects Registry; Arizona Birth Defects Monitoring Program; Arkansas Reproductive Health Monitoring System; California Birth Defects Monitoring Program; Colorado Responds to Children with Special Needs Section; Delaware Birth Defects Registry; Florida Birth Defects Registry; Metropolitan Atlanta Congenital Defects Program; Hawaii Birth Defects Program; Illinois Adverse Pregnancy Outcomes Reporting System; Indiana Birth Defects and Problems Registry; Iowa Registry for Congenital and Inherited Disorders; Kansas Birth Defects Program; Kentucky Birth Surveillance Registry; Louisiana Birth Defects Monitoring Network; Maine CDC Birth Defects Program; Maryland Birth Defects Reporting and Information System; Massachusetts Birth Defects Monitoring Program; Michigan Birth Defects Registry; Minnesota Birth Defects Information System; Mississippi Birth Defects Surveillance Registry; Missouri Birth Defect Surveillance System; Nebraska Birth Defect Registry; Nevada Birth Outcomes Monitoring System; New Jersey Special Child Health Services Registry; New Mexico Birth Defects Prevention and Surveillance System; New York State Birth Defects Registry; North Carolina Birth Defects Monitoring Program; Ohio Connections for Children with Special Needs; Oklahoma Birth Defect Registry; Oregon Birth Anomalies Surveillance System; Puerto Rico Birth Defects Surveillance and Prevention System; Rhode Island Birth Defects Program; South Carolina Birth Defects Program; Tennessee Birth Defects Surveillance System; Texas Birth Defects Epidemiology and Surveillance Branch; Utah Birth Defect Network; Vermont Birth Information Network; Washington State Birth Defects Surveillance System; West Virginia Birth Defects Surveillance System; Wisconsin Birth Defect Prevention and Surveillance System; and the U.S. Department of Defense Birth and Infant Health Registry. S1 Birth Defects Research 111: S1-S180 (2019)

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  • STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA

    Major Birth Defects Data from Population-based Birth Defects Surveillance Programs in the United States, 2012-2016

    The introduction, data collection procedure, and birth defects codes for the state-specific birth defects data are available in the article, “Population-based birth defects data in the United States, 2012-2016: A focus on abdominal wall defects.”

    Additional information and program contacts on population-based birth defects surveillance programs are available on page S126-S180.

    The state-specific birth defects tables were prepared by the National Center on Birth Defects and Developmental Disabilities, Centers for Disease Control and Prevention and approved by the state programs in September 2019.

    The 42 population-based birth defects programs contributing data include: Alaska Birth Defects Registry; Arizona Birth Defects Monitoring Program; Arkansas Reproductive Health Monitoring System; California Birth Defects Monitoring Program; Colorado Responds to Children with Special Needs Section; Delaware Birth Defects Registry; Florida Birth Defects Registry; Metropolitan Atlanta Congenital Defects Program; Hawaii Birth Defects Program; Illinois Adverse Pregnancy Outcomes Reporting System; Indiana Birth Defects and Problems Registry; Iowa Registry for Congenital and Inherited Disorders; Kansas Birth Defects Program; Kentucky Birth Surveillance Registry; Louisiana Birth Defects Monitoring Network; Maine CDC Birth Defects Program; Maryland Birth Defects Reporting and Information System; Massachusetts Birth Defects Monitoring Program; Michigan Birth Defects Registry; Minnesota Birth Defects Information System; Mississippi Birth Defects Surveillance Registry; Missouri Birth Defect Surveillance System; Nebraska Birth Defect Registry; Nevada Birth Outcomes Monitoring System; New Jersey Special Child Health Services Registry; New Mexico Birth Defects Prevention and Surveillance System; New York State Birth Defects Registry; North Carolina Birth Defects Monitoring Program; Ohio Connections for Children with Special Needs; Oklahoma Birth Defect Registry; Oregon Birth Anomalies Surveillance System; Puerto Rico Birth Defects Surveillance and Prevention System; Rhode Island Birth Defects Program; South Carolina Birth Defects Program; Tennessee Birth Defects Surveillance System; Texas Birth Defects Epidemiology and Surveillance Branch; Utah Birth Defect Network; Vermont Birth Information Network; Washington State Birth Defects Surveillance System; West Virginia Birth Defects Surveillance System; Wisconsin Birth Defect Prevention and Surveillance System; and the U.S. Department of Defense Birth and Infant Health Registry.

    S1

    Birth Defects Research 111: S1-S180 (2019)

  • AlaskaBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)AlaskaBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus

  • AlaskaBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Renal agenesis/hypoplasia 2410.0

  • AlaskaBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)AlaskaBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesTrisomy 13

  • ArizonaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)ArizonaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 241.3

    52.4

    382.2

    21.2

    83.3

    781.8

    Anophthalmia/microphthalmia 221.2

    73.3

    201.1

    42.5

    72.9

    601.4

    Anotia/microtia 221.2

    52.4

    362.0

    31.9

    104.1

    761.8

    Aortic valve stenosis 271.5

    00.0

    231.3

    31.9

    62.5

    601.4

    Atrioventricular septal defect(Endocardial cushion defect)

    874.7

    125.7

    864.9

    42.5

    177.0

    2074.8

    Biliary atresia 100.5

    00.0

    50.3

    10.6

    10.4

    170.4

    Bladder exstrophy 30.2

    00.0

    20.1

    00.0

    00.0

    50.1

    Choanal atresia 201.1

    31.4

    140.8

    00.0

    10.4

    380.9

    Cleft lip alone 764.1

    62.9

    482.7

    53.1

    156.1

    1503.5

    Cleft lip with cleft palate 1276.9

    167.6

    1056.0

    74.3

    4418.0

    3007.0

    Cleft palate alone 1307.1

    157.1

    985.6

    138.1

    249.8

    2816.6

    Coarctation of the aorta 854.6

    94.3

    844.8

    10.6

    166.5

    1954.5

    Common truncus (truncus arteriosus) 140.8

    10.5

    80.5

    31.9

    00.0

    260.6

    Congenital cataract 140.8

    31.4

    140.8

    10.6

    41.6

    360.8

    Diaphragmatic hernia 532.9

    41.9

    523.0

    63.7

    93.7

    1242.9

    Double outlet right ventricle 392.1

    62.9

    583.3

    53.1

    145.7

    1222.8

    Ebstein anomaly 120.7

    00.0

    120.7

    10.6

    52.0

    300.7

    Encephalocele 140.8

    31.4

    150.9

    00.0

    20.8

    340.8

    Esophageal atresia/tracheoesophagealfistula

    442.4

    10.5

    482.7

    42.5

    104.1

    1082.5

    Gastroschisis 1045.7

    157.1

    1247.1

    74.3

    3614.7

    2876.7

    Holoprosencephaly 120.7

    41.9

    140.8

    00.0

    20.8

    320.7

    Hypoplastic left heart syndrome 502.7

    73.3

    372.1

    10.6

    41.6

    992.3

    Interrupted aortic arch 160.9

    31.4

    140.8

    10.6

    31.2

    370.9

    Limb deficiencies (reduction defects) 553.0

    146.7

    653.7

    31.9

    104.1

    1473.4

    Omphalocele 492.7

    94.3

    442.5

    42.5

    10.4

    1082.5

    Pulmonary valve atresia and stenosis 613.3

    21.0

    462.6

    53.1

    93.7

    1232.9

    Pulmonary valve atresia 422.3

    83.8

    392.2

    63.7

    197.8

    1142.7

    Single ventricle 110.6

    31.4

    150.9

    00.0

    20.8

    310.7

    Spina bifida without anencephalus 563.0

    83.8

    502.8

    42.5

    156.1

    1343.1

    Tetralogy of Fallot 764.1

    94.3

    502.8

    85.0

    229.0

    1663.9

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S5

    Birth Defects Research 111: S1-S180 (2019)

  • ArizonaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Total anomalous pulmonary venousconnection

    201.1

    21.0

    372.1

    42.5

    62.5

    691.6

    Transposition of the great arteries(TGA)

    603.3

    31.4

    492.8

    53.1

    41.6

    1212.8

    Dextro-transposition of great arteries(d-TGA)

    462.5

    21.0

    352.0

    53.1

    20.8

    902.1

    Tricuspid valve atresia and stenosis 00.0

    00.0

    00.0

    00.0

    20.8

    20.0

    Tricuspid valve atresia 110.6

    21.0

    160.9

    31.9

    52.0

    370.9

    Trisomy 13 221.2

    94.3

    201.1

    00.0

    31.2

    541.3

    Trisomy 18 422.3

    52.4

    422.4

    42.5

    62.5

    1012.4

    Trisomy 21 (Down syndrome) 25714.0

    3516.6

    26415.0

    2918.0

    3715.1

    62414.6

    Total live births 183,894 21,025 175,823 16,124 24,429 428,584

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S6

    Birth Defects Research 111: S1-S180 (2019)

  • ArizonaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)ArizonaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 281

    7.650.8

    2876.7

    Trisomy 13 351.0

    193.1

    541.3

    Trisomy 18 521.4

    467.5

    1012.4

    Trisomy 21 (Down syndrome) 3218.7

    30149.2

    62414.6

    Total live births 367,432 61,124 428,584

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S7

    Birth Defects Research 111: S1-S180 (2019)

  • ArkansasBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)ArkansasBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 151.4

    41.4

    32.0

    37.0

    00.0

    251.6

    Anophthalmia/microphthalmia 151.4

    41.4

    32.0

    37.0

    00.0

    261.7

    Anotia/microtia 252.4

    41.4

    117.2

    00.0

    00.0

    412.7

    Aortic valve stenosis 363.5

    31.1

    85.2

    00.0

    17.5

    513.3

    Atrial septal defect 35133.9

    10839.1

    5636.6

    2353.8

    430.2

    56036.6

    Atrioventricular septal defect(Endocardial cushion defect)

    767.3

    196.9

    106.5

    49.4

    00.0

    1117.3

    Biliary atresia 60.6

    20.7

    00.0

    00.0

    00.0

    80.5

    Bladder exstrophy 10.1

    10.4

    00.0

    00.0

    00.0

    20.1

    Choanal atresia 20.2

    00.0

    10.7

    12.3

    00.0

    40.3

    Cleft lip alone 525.0

    62.2

    32.0

    12.3

    00.0

    654.2

    Cleft lip with cleft palate 827.9

    103.6

    127.8

    49.4

    00.0

    1117.3

    Cleft palate alone 817.8

    165.8

    127.8

    12.3

    00.0

    1147.4

    Cloacal exstrophy 00.0

    10.4

    10.7

    00.0

    00.0

    20.1

    Clubfoot 18718.1

    3813.7

    2818.3

    818.7

    430.2

    27417.9

    Coarctation of the aorta 737.1

    124.3

    106.5

    49.4

    00.0

    1006.5

    Common truncus (truncus arteriosus) 50.5

    10.4

    00.0

    12.3

    00.0

    70.5

    Congenital cataract 302.9

    72.5

    63.9

    24.7

    00.0

    463.0

    Congenital posterior urethral valves 71.3

    53.6

    11.3

    00.0

    00.0

    151.9

    1

    Craniosynostosis 767.3

    124.3

    63.9

    12.3

    215.1

    1006.5

    Deletion 22q11.2 60.6

    10.4

    10.7

    00.0

    00.0

    80.5

    Diaphragmatic hernia 363.5

    51.8

    85.2

    12.3

    17.5

    523.4

    Double outlet right ventricle 191.8

    82.9

    85.2

    12.3

    00.0

    382.5

    Ebstein anomaly 121.2

    00.0

    10.7

    00.0

    00.0

    140.9

    Encephalocele 70.7

    62.2

    10.7

    12.3

    00.0

    171.1

    Esophageal atresia/tracheoesophagealfistula

    212.0

    31.1

    21.3

    12.3

    00.0

    271.8

    Gastroschisis 727.0

    124.3

    117.2

    37.0

    322.6

    1056.9

    Holoprosencephaly 141.4

    31.1

    00.0

    24.7

    00.0

    201.3

    Hypoplastic left heart syndrome 333.2

    82.9

    21.3

    49.4

    00.0

    493.2

    Hypospadias 50194.2

    12186.3

    2633.4

    1046.0

    114.4

    68186.9

    1

    Interrupted aortic arch 30.3

    20.7

    21.3

    12.3

    00.0

    90.6

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S8

    Birth Defects Research 111: S1-S180 (2019)

  • ArkansasBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 343.3

    103.6

    53.3

    12.3

    215.1

    533.5

    Omphalocele 242.3

    51.8

    53.3

    00.0

    00.0

    342.2

    Pulmonary valve atresia and stenosis 13713.2

    3412.3

    127.8

    49.4

    00.0

    19312.6

    Pulmonary valve atresia 101.0

    31.1

    00.0

    00.0

    00.0

    130.8

    Rectal and large intestinalatresia/stenosis

    363.5

    165.8

    74.6

    12.3

    00.0

    654.2

    Renal agenesis/hypoplasia 252.4

    31.1

    53.3

    12.3

    215.1

    362.4

    Single ventricle 60.6

    20.7

    10.7

    00.0

    00.0

    90.6

    Small intestinal atresia/stenosis 454.3

    82.9

    63.9

    00.0

    00.0

    634.1

    Spina bifida without anencephalus 343.3

    72.5

    95.9

    12.3

    00.0

    533.5

    Tetralogy of Fallot 444.3

    165.8

    53.3

    12.3

    17.5

    674.4

    Total anomalous pulmonary venousconnection

    141.4

    93.3

    32.0

    12.3

    00.0

    291.9

    Transposition of the great arteries(TGA)

    292.8

    41.4

    42.6

    12.3

    17.5

    412.7

    Dextro-transposition of great arteries(d-TGA)

    212.0

    31.1

    32.0

    12.3

    17.5

    302.0

    Tricuspid valve atresia 30.3

    10.4

    10.7

    00.0

    00.0

    50.3

    Trisomy 13 90.9

    41.4

    00.0

    12.3

    00.0

    140.9

    Trisomy 18 181.7

    20.7

    53.3

    24.7

    00.0

    281.8

    Trisomy 21 (Down syndrome) 11611.2

    3311.9

    3623.5

    511.7

    00.0

    19212.5

    Turner syndrome 61.2

    10.7

    00.0

    14.8

    00.0

    81.1

    2

    Ventricular septal defect 57355.4

    12244.1

    10065.3

    1330.4

    322.6

    83554.6

    Total live births 103,452 27,648 15,305 4,272 1,326 153,032

    Male live births 53,197 14,024 7,778 2,173 696 78,390

    Female live births 50,255 13,624 7,527 2,099 630 74,642

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S9

    Birth Defects Research 111: S1-S180 (2019)

  • ArkansasBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)ArkansasBirth Defects Counts and Prevalence 2012 - 2015 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 104

    7.500.0

    1056.9

    Trisomy 13 100.7

    42.8

    140.9

    Trisomy 18 211.5

    64.2

    281.8

    Trisomy 21 (Down syndrome) 1148.2

    7753.8

    19212.5

    Total live births 138,685 14,317 153,032

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S10

    Birth Defects Research 111: S1-S180 (2019)

  • CaliforniaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)CaliforniaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus

  • CaliforniaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Omphalocele 162.0

    74.6

    281.5

  • CaliforniaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)CaliforniaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 180

    6.5

  • ColoradoBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)ColoradoBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 80.4

    32.0

    70.8

    00.0

    00.0

    341.0

    Anophthalmia/microphthalmia 281.4

    10.7

    141.6

    21.6

    14.7

    662.0

    Anotia/microtia 190.9

    10.7

    394.3

    43.1

    00.0

    962.9

    Aortic valve stenosis 522.6

    32.0

    252.8

    10.8

    00.0

    962.9

    Atrial septal defect 1,95496.3

    187127.1

    990110.1

    11288.1

    31145.5

    4,384133.2

    Atrioventricular septal defect(Endocardial cushion defect)

    643.2

    85.4

    293.2

    43.1

    00.0

    1123.4

    Biliary atresia 241.2

    00.0

    91.0

    00.0

    14.7

    652.0

    Bladder exstrophy 50.2

    00.0

    20.2

    00.0

    00.0

    90.3

    Choanal atresia 311.5

    10.7

    121.3

    10.8

    00.0

    621.9

    Cleft lip alone 803.9

    106.8

    404.4

    32.4

    14.7

    1434.3

    Cleft lip with cleft palate 1406.9

    74.8

    748.2

    64.7

    29.4

    2517.6

    Cleft palate alone 1718.4

    96.1

    788.7

    2116.5

    418.8

    3039.2

    Clubfoot 29614.6

    138.8

    13114.6

    1411.0

    523.5

    64219.5

    Coarctation of the aorta 1879.2

    117.5

    728.0

    43.1

    00.0

    2828.6

    Common truncus (truncus arteriosus) 160.8

    10.7

    60.7

    00.0

    00.0

    270.8

    Congenital cataract 412.0

    00.0

    171.9

    32.4

    00.0

    832.5

    Congenital posterior urethral valves 252.4

    34.0

    61.3

    23.1

    00.0

    694.1

    1

    Deletion 22q11.2 211.3

    21.7

    131.8

    00.0

    15.9

    401.5

    Diaphragmatic hernia 522.6

    64.1

    232.6

    21.6

    00.0

    842.6

    Double outlet right ventricle 291.4

    64.1

    232.6

    32.4

    00.0

    672.0

    Ebstein anomaly 150.7

    00.0

    60.7

    21.6

    00.0

    240.7

    Encephalocele 160.8

    32.0

    80.9

    10.8

    00.0

    361.1

    Esophageal atresia/tracheoesophagealfistula

    653.2

    21.4

    323.6

    43.1

    00.0

    1334.0

    Gastroschisis 763.7

    42.7

    394.3

    32.4

    628.2

    1444.4

    Holoprosencephaly 130.6

    10.7

    91.0

    21.6

    00.0

    260.8

    Hypoplastic left heart syndrome 522.6

    32.0

    262.9

    10.8

    00.0

    932.8

    Hypospadias 1,103106.3

    85113.0

    28361.6

    4874.2

    12108.8

    1,924114.3

    1

    Interrupted aortic arch 512.5

    106.8

    293.2

    21.6

    00.0

    962.9

    Limb deficiencies (reduction defects) 743.6

    53.4

    374.1

    10.8

    00.0

    1494.5

    Omphalocele 301.5

    53.4

    151.7

    00.0

    14.7

    802.4

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S14

    Birth Defects Research 111: S1-S180 (2019)

  • ColoradoBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Pulmonary valve atresia and stenosis 1366.7

    1610.9

    697.7

    32.4

    314.1

    2377.2

    Pulmonary valve atresia 341.7

    64.1

    252.8

    00.0

    29.4

    722.2

    Rectal and large intestinalatresia/stenosis

    653.2

    85.4

    444.9

    53.9

    29.4

    1725.2

    Renal agenesis/hypoplasia 844.1

    85.4

    353.9

    43.1

    29.4

    2116.4

    Single ventricle 140.7

    21.4

    50.6

    00.0

    14.7

    250.8

    Small intestinal atresia/stenosis 793.9

    85.4

    546.0

    64.7

    14.7

    1795.4

    Spina bifida without anencephalus 492.4

    53.4

    303.3

    32.4

    14.7

    1013.1

    Tetralogy of Fallot 592.9

    42.7

    384.2

    10.8

    314.1

    1093.3

    Total anomalous pulmonary venousconnection

    211.0

    21.4

    232.6

    32.4

    00.0

    491.5

    Transposition of the great arteries(TGA)

    512.5

    64.1

    171.9

    53.9

    00.0

    812.5

    Dextro-transposition of great arteries(d-TGA)

    432.1

    64.1

    141.6

    53.9

    00.0

    702.1

    Tricuspid valve atresia and stenosis 251.2

    42.7

    111.2

    00.0

    00.0

    441.3

    Tricuspid valve atresia 231.1

    42.7

    111.2

    00.0

    00.0

    411.2

    Trisomy 13 110.5

    21.4

    80.9

    10.8

    00.0

    842.6

    Trisomy 18 201.0

    32.0

    60.7

    21.6

    00.0

    1364.1

    Trisomy 21 (Down syndrome) 24912.3

    2819.0

    18820.9

    1310.2

    29.4

    73322.3

    Turner syndrome 222.2

    45.6

    71.6

    11.6

    19.7

    875.4

    2

    Ventricular septal defect 84741.7

    7148.2

    46952.1

    4031.5

    1675.1

    1,80654.9

    Total live births 202,944 14,718 89,938 12,713 2,130 329,245 3

    Male live births 103,792 7,523 45,918 6,466 1,103 168,285

    Female live births 99,148 7,194 44,017 6,247 1,027 160,952

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S15

    Birth Defects Research 111: S1-S180 (2019)

  • ColoradoBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)ColoradoBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 132

    4.961.0

    1444.4

    Trisomy 13 261.0

    152.5

    842.6

    Trisomy 18 481.8

    294.8

    1364.1

    Trisomy 21 (Down syndrome) 2559.5

    26644.4

    73322.3

    Total live births 269,205 59,915 329,245 3

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.3. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S16

    Birth Defects Research 111: S1-S180 (2019)

  • DelawareBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)DelawareBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 31.1

    10.7

    00.0

    00.0

    00.0

    40.8

    Anophthalmia/microphthalmia 10.4

    53.5

    00.0

    00.0

    00.0

    61.1

    Anotia/microtia 82.9

    42.8

    79.8

    26.9

    00.0

    214.0

    Aortic valve stenosis 72.5

    00.0

    45.6

    13.5

    00.0

    122.3

    Atrial septal defect 8430.0

    4330.5

    3245.0

    827.7

    00.0

    17032.3

    1

    Atrioventricular septal defect(Endocardial cushion defect)

    186.4

    117.8

    1014.1

    00.0

    00.0

    407.6

    Biliary atresia 00.0

    10.7

    00.0

    00.0

    00.0

    30.6

    Bladder exstrophy 20.7

    10.7

    00.0

    00.0

    00.0

    30.6

    Choanal atresia 20.7

    21.4

    00.0

    00.0

    00.0

    40.8

    Cleft lip alone 82.9

    10.7

    57.0

    13.5

    00.0

    152.8

    Cleft lip with cleft palate 165.7

    42.8

    45.6

    26.9

    00.0

    275.1

    Cleft palate alone 186.4

    107.1

    45.6

    13.5

    00.0

    336.3

    2

    Cloacal exstrophy 00.0

    10.7

    00.0

    00.0

    00.0

    10.2

    Clubfoot 4315.3

    1611.4

    811.3

    310.4

    00.0

    7313.9

    Coarctation of the aorta 165.7

    75.0

    45.6

    413.8

    00.0

    315.9

    Common truncus (truncus arteriosus) 10.4

    10.7

    00.0

    00.0

    00.0

    20.4

    Congenital cataract 62.1

    21.4

    11.4

    26.9

    00.0

    112.1

    Congenital posterior urethral valves 42.8

    68.5

    00.0

    16.5

    00.0

    114.1

    3

    Craniosynostosis 165.7

    85.7

    22.8

    00.0

    00.0

    285.3

    Deletion 22q11.2 51.8

    10.7

    00.0

    00.0

    00.0

    61.1

    Diaphragmatic hernia 51.8

    00.0

    11.4

    13.5

    00.0

    71.3

    Double outlet right ventricle 20.7

    32.1

    11.4

    13.5

    00.0

    81.5

    Ebstein anomaly 20.7

    00.0

    00.0

    00.0

    00.0

    20.4

    Encephalocele 31.1

    21.4

    00.0

    00.0

    00.0

    50.9

    Esophageal atresia/tracheoesophagealfistula

    51.8

    10.7

    00.0

    00.0

    00.0

    61.1

    Gastroschisis 155.4

    107.1

    45.6

    26.9

    00.0

    326.1

    Holoprosencephaly 10.4

    32.1

    34.2

    00.0

    00.0

    71.3

    Hypoplastic left heart syndrome 82.9

    10.7

    22.8

    00.0

    00.0

    112.1

    Hypospadias 144100.7

    6287.5

    1130.8

    1491.3

    00.0

    23587.8

    4

    Interrupted aortic arch 00.0

    00.0

    11.7

    00.0

    00.0

    10.2

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S17

    Birth Defects Research 111: S1-S180 (2019)

  • DelawareBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 217.5

    128.5

    45.6

    310.4

    00.0

    407.6

    Omphalocele 41.4

    75.0

    34.2

    00.0

    00.0

    142.7

    Pulmonary valve atresia and stenosis 4014.3

    3424.1

    811.3

    13.5

    00.0

    8516.1

    Pulmonary valve atresia 72.5

    42.8

    34.2

    00.0

    00.0

    142.7

    Rectal and large intestinalatresia/stenosis

    134.6

    75.0

    11.4

    26.9

    00.0

    234.4

    Renal agenesis/hypoplasia 269.3

    85.7

    22.8

    13.5

    00.0

    377.0

    Single ventricle 00.0

    10.7

    11.4

    00.0

    00.0

    20.4

    Small intestinal atresia/stenosis 103.6

    85.7

    34.2

    00.0

    00.0

    214.0

    Spina bifida without anencephalus 20.7

    64.3

    57.0

    00.0

    00.0

    132.5

    Tetralogy of Fallot 113.9

    75.0

    11.4

    00.0

    00.0

    193.6

    Total anomalous pulmonary venousconnection

    31.1

    21.4

    57.0

    13.5

    00.0

    112.1

    Transposition of the great arteries(TGA)

    124.3

    21.4

    34.2

    13.5

    00.0

    183.4

    Dextro-transposition of great arteries(d-TGA)

    10.4

    00.0

    11.4

    00.0

    00.0

    20.4

    Tricuspid valve atresia and stenosis 20.7

    32.1

    00.0

    13.5

    00.0

    61.1

    Tricuspid valve atresia 20.7

    10.7

    00.0

    13.5

    00.0

    40.8

    Trisomy 13 20.7

    21.4

    22.8

    13.5

    00.0

    71.3

    Trisomy 18 51.8

    10.7

    68.4

    26.9

    00.0

    142.7

    Trisomy 21 (Down syndrome) 4014.3

    1812.8

    1723.9

    413.8

    00.0

    8015.2

    Turner syndrome 32.2

    11.4

    12.8

    00.0

    00.0

    62.3

    5

    Ventricular septal defect 23282.8

    9265.3

    5476.0

    2483.1

    00.0

    41278.2

    6

    Total live births 28,036 14,088 7,107 2,889 111 52,695

    Male live births 14,305 7,086 3,569 1,533 39 26,776

    Female live births 13,731 7,002 3,538 1,356 72 25,919

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S18

    Birth Defects Research 111: S1-S180 (2019)

  • DelawareBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)DelawareBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 32

    7.100.0

    326.1

    Trisomy 13 61.3

    11.3

    71.3

    Trisomy 18 10.2

    1316.5

    142.7

    Trisomy 21 (Down syndrome) 378.3

    4354.6

    8015.2

    Total live births 44,814 7,881 52,695

    Notes1. Data for this condition include atrial septal fenestrations and exclude atrial septal defects that self-close (not present after a month), which areconsidered patent foramen ovales.2. Data for this condition include Pierre Robin anomalies with cleft palate.3. Data for this condition include only cases involving surgical intervention. Data for this condition include male and unknown gender cases only.Prevalence is calculated per 10,000 male live births.4. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.5. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.6. Data for this condition include probable cases only if the defect was found prenatally and the fetus died without a confirmatory autopsy.

    General comments*Data for totals include unknown and/or other.-Data for all heart defects require an echocardiogram report.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S19

    Birth Defects Research 111: S1-S180 (2019)

  • FloridaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)FloridaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 450.9

    231.0

    250.8

  • FloridaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 1823.8

    883.7

    993.2

    72.2

  • FloridaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)FloridaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 432

    4.7130.7

    4454.1

    3

    Trisomy 13 740.8

    321.8

    1061.0

    Trisomy 18 1061.2

    995.6

    2051.9

    Trisomy 21 (Down syndrome) 6807.5

    70439.8

    1,38412.7

    Total live births 912,720 176,958 1,089,749 7

    Notes1. Data for this condition include canal type atrioventricular septal defect.2. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.3. Data for this condition may differ from previous reports due to ICD-9-CM coding system changes.4. Data for this condition include congenital tricuspid stenosis.5. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.6. Data for this condition include probable cases.7. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S22

    Birth Defects Research 111: S1-S180 (2019)

  • Georgia (Metropolitan Atlanta Congenital Defects Program)Birth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)Georgia (Metropolitan Atlanta Congenital Defects Program)Birth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 102.1

    121.6

    61.8

    10.7

    00.0

    362.0

    Anophthalmia/microphthalmia 102.1

    91.2

    61.8

    00.0

    00.0

    281.6

    Anotia/microtia 112.3

    50.7

    103.0

    42.7

    00.0

    341.9

    Aortic valve stenosis 153.1

    30.4

    61.8

    10.7

    00.0

    271.5

    Atrial septal defect 6513.6

    17623.7

    3911.7

    1711.5

    00.0

    33118.7

    Atrioventricular septal defect(Endocardial cushion defect)

    234.8

    496.6

    103.0

    42.7

    00.0

    995.6

    Biliary atresia 20.4

    10.1

    20.6

    00.0

    00.0

    60.3

    Bladder exstrophy 20.4

    10.1

    00.0

    00.0

    00.0

    30.2

    Choanal atresia 10.2

    70.9

    20.6

    00.0

    00.0

    110.6

    Cleft lip alone 204.2

    141.9

    72.1

    42.7

    00.0

    482.7

    Cleft lip with cleft palate 265.4

    304.0

    185.4

    106.7

    00.0

    995.6

    Cleft palate alone 245.0

    283.8

    123.6

    128.1

    00.0

    834.7

    Cloacal exstrophy 00.0

    10.1

    00.0

    10.7

    00.0

    20.1

    Clubfoot 459.4

    9012.1

    267.8

    1912.8

    00.0

    20411.5

    Coarctation of the aorta 367.5

    304.0

    164.8

    64.0

    00.0

    945.3

    Common truncus (truncus arteriosus) 10.2

    40.5

    10.3

    10.7

    00.0

    80.5

    Congenital cataract 61.3

    91.2

    10.3

    21.3

    00.0

    221.2

    Congenital posterior urethral valves 20.8

    174.5

    31.8

    11.3

    00.0

    262.9

    1

    Craniosynostosis 204.2

    141.9

    82.4

    53.4

    00.0

    553.1

    Deletion 22q11.2 40.8

    81.1

    51.5

    10.7

    00.0

    201.1

    Diaphragmatic hernia 163.3

    202.7

    82.4

    21.3

    00.0

    583.3

    Double outlet right ventricle 51.0

    202.7

    92.7

    42.7

    00.0

    422.4

    Ebstein anomaly 00.0

    50.7

    20.6

    21.3

    00.0

    90.5

    Encephalocele 00.0

    40.5

    20.6

    21.3

    00.0

    110.6

    Esophageal atresia/tracheoesophagealfistula

    132.7

    172.3

    20.6

    00.0

    00.0

    341.9

    Gastroschisis 194.0

    192.6

    154.5

    10.7

    00.0

    613.4

    Holoprosencephaly 81.7

    121.6

    10.3

    21.3

    00.0

    301.7

    Hypoplastic left heart syndrome 153.1

    172.3

    61.8

    00.0

    00.0

    422.4

    Hypospadias 17170.1

    18449.2

    4426.1

    3343.6

    1178.6

    51957.8

    1

    Interrupted aortic arch 30.6

    40.5

    20.6

    00.0

    00.0

    130.7

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S23

    Birth Defects Research 111: S1-S180 (2019)

  • Georgia (Metropolitan Atlanta Congenital Defects Program)Birth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 142.9

    212.8

    82.4

    21.3

    00.0

    533.0

    Omphalocele 81.7

    223.0

    61.8

    21.3

    00.0

    492.8

    Pulmonary valve atresia and stenosis 377.7

    496.6

    206.0

    96.1

    00.0

    1337.5

    Pulmonary valve atresia 102.1

    202.7

    41.2

    42.7

    00.0

    382.1

    Rectal and large intestinalatresia/stenosis

    204.2

    263.5

    154.5

    32.0

    00.0

    653.7

    Renal agenesis/hypoplasia 224.6

    364.9

    72.1

    64.0

    00.0

    834.7

    Single ventricle 20.4

    20.3

    10.3

    10.7

    00.0

    70.4

    Small intestinal atresia/stenosis 132.7

    192.6

    61.8

    10.7

    00.0

    442.5

    Spina bifida without anencephalus 173.5

    131.8

    82.4

    32.0

    00.0

    512.9

    Tetralogy of Fallot 204.2

    293.9

    61.8

    74.7

    00.0

    693.9

    Total anomalous pulmonary venousconnection

    61.3

    70.9

    41.2

    42.7

    00.0

    231.3

    Transposition of the great arteries(TGA)

    132.7

    152.0

    92.7

    10.7

    187.7

    502.8

    Dextro-transposition of great arteries(d-TGA)

    122.5

    131.8

    82.4

    10.7

    187.7

    452.5

    Tricuspid valve atresia and stenosis 61.3

    131.8

    72.1

    32.0

    00.0

    291.6

    Tricuspid valve atresia 51.0

    50.7

    30.9

    32.0

    00.0

    160.9

    Trisomy 13 102.1

    91.2

    41.2

    10.7

    00.0

    291.6

    Trisomy 18 81.7

    172.3

    51.5

    32.0

    00.0

    442.5

    Trisomy 21 (Down syndrome) 5611.7

    8010.8

    6118.3

    138.8

    00.0

    23813.4

    Turner syndrome 73.0

    92.5

    00.0

    22.8

    00.0

    232.6

    2

    Ventricular septal defect 27958.3

    29639.9

    20862.5

    7147.9

    187.7

    96554.5

    Total live births 47,889 74,110 33,258 14,821 114 177,217

    Male live births 24,389 37,396 16,848 7,575 56 89,860

    Female live births 23,500 36,714 16,410 7,246 58 87,356

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S24

    Birth Defects Research 111: S1-S180 (2019)

  • Georgia (Metropolitan Atlanta Congenital Defects Program)Birth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)Georgia (Metropolitan Atlanta Congenital Defects Program)Birth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 54

    3.961.6

    613.4

    Trisomy 13 171.2

    123.1

    291.6

    Trisomy 18 191.4

    225.7

    442.5

    Trisomy 21 (Down syndrome) 1118.0

    12432.3

    23813.4

    Total live births 138,850 38,345 177,217

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.

    General comments*Data for totals include unknown and/or other.-Cases for which the date of delivery was unknown are included in the year of their last known prenatal test.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S25

    Birth Defects Research 111: S1-S180 (2019)

  • HawaiiBirth Defects Counts and Prevalence 2012 (Prevalence per 10,000 Live Births)HawaiiBirth Defects Counts and Prevalence 2012 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic Total* Notes

    Anencephalus 25.5

    00.0

    00.0

    10.9

    42.1

    Anotia/microtia 12.7

    00.0

    00.0

    00.0

    10.5

    Atrial septal defect 719.2

    00.0

    413.4

    1815.4

    3518.4

    Atrioventricular septal defect(Endocardial cushion defect)

    12.7

    00.0

    13.4

    32.6

    52.6

    Biliary atresia 12.7

    00.0

    00.0

    21.7

    31.6

    Bladder exstrophy 12.7

    00.0

    00.0

    00.0

    10.5

    Choanal atresia 12.7

    00.0

    00.0

    00.0

    10.5

    Cleft lip alone 25.5

    00.0

    00.0

    43.4

    73.7

    Cleft lip with cleft palate 12.7

    00.0

    00.0

    65.1

    84.2

    Cleft palate alone 38.2

    00.0

    26.7

    86.8

    147.4

    Coarctation of the aorta 12.7

    00.0

    00.0

    32.6

    42.1

    Ebstein anomaly 00.0

    00.0

    00.0

    10.9

    10.5

    Encephalocele 00.0

    00.0

    00.0

    21.7

    21.1

    Esophageal atresia/tracheoesophagealfistula

    12.7

    00.0

    00.0

    32.6

    52.6

    Gastroschisis 25.5

    00.0

    00.0

    97.7

    126.3

    Hypoplastic left heart syndrome 00.0

    00.0

    00.0

    21.7

    31.6

    Hypospadias 632.7

    00.0

    213.1

    4066.8

    5455.8

    1

    Omphalocele 00.0

    00.0

    13.4

    32.6

    42.1

    Pulmonary valve atresia and stenosis 513.7

    00.0

    13.4

    54.3

    126.3

    Pulmonary valve atresia 00.0

    00.0

    00.0

    21.7

    21.1

    Rectal and large intestinalatresia/stenosis

    38.2

    00.0

    00.0

    86.8

    126.3

    Renal agenesis/hypoplasia 12.7

    00.0

    00.0

    65.1

    84.2

    Spina bifida without anencephalus 00.0

    00.0

    00.0

    10.9

    10.5

    Tetralogy of Fallot 12.7

    00.0

    00.0

    10.9

    21.1

    Total anomalous pulmonary venousconnection

    00.0

    00.0

    00.0

    21.7

    21.1

    Transposition of the great arteries(TGA)

    00.0

    122.0

    13.4

    65.1

    84.2

    Tricuspid valve atresia and stenosis 00.0

    00.0

    13.4

    32.6

    42.1

    Tricuspid valve atresia 00.0

    00.0

    13.4

    32.6

    42.1

    Trisomy 13 00.0

    00.0

    00.0

    21.7

    21.1

    Trisomy 18 411.0

    00.0

    13.4

    65.1

    157.9

    Trisomy 21 (Down syndrome) 513.7

    00.0

    26.7

    1412.0

    2915.3

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S26

    Birth Defects Research 111: S1-S180 (2019)

  • HawaiiBirth Defects Counts and Prevalence 2012 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic Total* Notes

    Turner syndrome 15.5

    00.0

    00.0

    11.8

    22.2

    2

    Ventricular septal defect 821.9

    00.0

    413.4

    2924.8

    5026.3

    Total live births 3,648 455 2,977 11,697 18,985

    Male live births 1,834 228 1,532 5,989 9,684

    Female live births 1,814 227 1,445 5,708 9,301

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S27

    Birth Defects Research 111: S1-S180 (2019)

  • HawaiiBirth Defects Counts and Prevalence 2012 (Prevalence per 10,000 Live Births)HawaiiBirth Defects Counts and Prevalence 2012 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 12

    7.700.0

    126.3

    Trisomy 13 10.6

    12.9

    21.1

    Trisomy 18 85.1

    720.6

    157.9

    Trisomy 21 (Down syndrome) 138.3

    1647.0

    2915.3

    Total live births 15,582 3,403 18,985

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S28

    Birth Defects Research 111: S1-S180 (2019)

  • IllinoisBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IllinoisBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 461.1

    181.4

    392.3

    91.9

    00.0

    1131.4

    Anophthalmia/microphthalmia 972.3

    332.5

    492.9

    71.4

    236.3

    1882.4

    Anotia/microtia 651.5

    141.1

    764.5

    91.9

    00.0

    1642.1

    Aortic valve stenosis 811.9

    251.9

    332.0

    81.7

    00.0

    1471.9

    Atrial septal defect 1,29830.8

    46135.2

    58134.5

    18838.8

    8145.2

    2,54232.3

    Atrioventricular septal defect(Endocardial cushion defect)

    2255.3

    826.3

    855.0

    153.1

    00.0

    4085.2

    1

    Biliary atresia 120.3

    80.6

    70.4

    71.4

    00.0

    340.4

    Bladder exstrophy 100.2

    00.0

    50.3

    20.4

    00.0

    170.2

    Choanal atresia 541.3

    181.4

    211.2

    40.8

    00.0

    971.2

    Cleft lip alone 1393.3

    312.4

    482.8

    112.3

    118.1

    2302.9

    Cleft lip with cleft palate 2365.6

    584.4

    1307.7

    183.7

    00.0

    4435.6

    Cleft palate alone 2616.2

    594.5

    824.9

    367.4

    236.3

    4405.6

    Cloacal exstrophy 120.3

    20.2

    40.2

    20.4

    00.0

    200.3

    Clubfoot 55513.2

    16912.9

    22913.6

    5711.8

    472.6

    1,01712.9

    Coarctation of the aorta 2105.0

    453.4

    865.1

    173.5

    236.3

    3604.6

    Common truncus (truncus arteriosus) 260.6

    50.4

    80.5

    20.4

    00.0

    410.5

    Congenital cataract 471.1

    282.1

    181.1

    71.4

    00.0

    1001.3

    Congenital posterior urethral valves 421.9

    203.0

    101.2

    41.6

    00.0

    761.9

    2

    Craniosynostosis 1824.3

    322.4

    855.0

    112.3

    00.0

    3103.9

    Deletion 22q11.2 441.0

    201.5

    130.8

    51.0

    00.0

    821.0

    Diaphragmatic hernia 1343.2

    221.7

    573.4

    102.1

    00.0

    2232.8

    Double outlet right ventricle 751.8

    292.2

    382.3

    71.4

    00.0

    1491.9

    Ebstein anomaly 230.5

    70.5

    211.2

    30.6

    00.0

    540.7

    Encephalocele 270.6

    120.9

    181.1

    40.8

    00.0

    620.8

    Esophageal atresia/tracheoesophagealfistula

    1283.0

    262.0

    392.3

    112.3

    118.1

    2052.6

    Gastroschisis 1423.4

    675.1

    744.4

    40.8

    118.1

    2883.7

    Holoprosencephaly 340.8

    211.6

    311.8

    20.4

    118.1

    891.1

    Hypoplastic left heart syndrome 892.1

    403.0

    342.0

    91.9

    118.1

    1732.2

    Hypospadias 1,55972.0

    41362.0

    26831.3

    13253.2

    14493.0

    2,38659.3

    2

    Interrupted aortic arch 220.5

    171.3

    120.7

    00.0

    00.0

    510.6

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S29

    Birth Defects Research 111: S1-S180 (2019)

  • IllinoisBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 1824.3

    775.9

    744.4

    153.1

    00.0

    3494.4

    Omphalocele 781.8

    362.7

    241.4

    61.2

    118.1

    1451.8

    Pulmonary valve atresia and stenosis 2235.3

    1007.6

    1166.9

    336.8

    118.1

    4746.0

    Pulmonary valve atresia 160.4

    90.7

    120.7

    20.4

    00.0

    390.5

    3

    Rectal and large intestinalatresia/stenosis

    1663.9

    433.3

    724.3

    173.5

    354.4

    3013.8

    Renal agenesis/hypoplasia 3007.1

    13110.0

    1398.3

    428.7

    00.0

    6127.8

    Single ventricle 190.5

    80.6

    100.6

    20.4

    00.0

    390.5

    Small intestinal atresia/stenosis 1192.8

    463.5

    633.7

    142.9

    118.1

    2433.1

    Spina bifida without anencephalus 1493.5

    393.0

    543.2

    102.1

    00.0

    2523.2

    Tetralogy of Fallot 1704.0

    644.9

    623.7

    245.0

    236.3

    3234.1

    Total anomalous pulmonary venousconnection

    330.8

    141.1

    311.8

    61.2

    00.0

    841.1

    Transposition of the great arteries(TGA)

    1323.1

    272.1

    442.6

    102.1

    00.0

    2142.7

    Dextro-transposition of great arteries(d-TGA)

    1102.6

    231.8

    332.0

    71.4

    00.0

    1732.2

    Tricuspid valve atresia and stenosis 340.8

    211.6

    241.4

    51.0

    00.0

    841.1

    4

    Tricuspid valve atresia 160.4

    80.6

    150.9

    20.4

    00.0

    410.5

    5

    Trisomy 13 451.1

    141.1

    241.4

    30.6

    00.0

    861.1

    Trisomy 18 1132.7

    312.4

    533.1

    153.1

    00.0

    2142.7

    Trisomy 21 (Down syndrome) 54612.9

    14911.4

    36421.6

    5210.7

    6108.9

    1,11814.2

    Turner syndrome 351.7

    101.5

    182.2

    20.8

    00.0

    651.7

    6

    Ventricular septal defect 1,99047.2

    55442.2

    94055.8

    23949.4

    13235.9

    3,73747.5

    7

    Total live births 421,754 131,148 168,475 48,405 551 787,160 8

    Male live births 216,614 66,596 85,671 24,797 284 402,622

    Female live births 205,132 64,543 82,797 23,608 267 384,513

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S30

    Birth Defects Research 111: S1-S180 (2019)

  • IllinoisBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IllinoisBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 275

    4.2130.9

    2883.7

    Trisomy 13 560.9

    302.2

    861.1

    Trisomy 18 1221.9

    906.6

    2142.7

    Trisomy 21 (Down syndrome) 5127.9

    60544.1

    1,11814.2

    Total live births 649,986 137,113 787,160 8

    Notes1. Data for this condition include inlet ventricular septal defects including common atrioventricular canal type ventricular septal defect.2. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.3. Data for this condition exclude cases with tetralogy of Fallot or cases with a ventricular septal defect.4. Data for this condition include tricuspid stenosis or hypoplasia.5. Data for this condition exclude tricuspid stenosis or hypoplasia.6. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.7. Data for this condition exclude probable cases, and inlet ventricular septal defects including common atrioventricular canal type ventricular septaldefects.8. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.-More complete hospital discharge data was made available beginning in 2013 which allowed for the identification of cases diagnosed at a later date.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S31

    Birth Defects Research 111: S1-S180 (2019)

  • IndianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IndianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 160.5

    20.4

    10.4

    11.0

    00.0

    200.5

    Anophthalmia/microphthalmia 230.7

    20.4

    20.7

    00.0

    00.0

    270.7

    Anotia/microtia 280.9

    51.1

    82.8

    43.9

    00.0

    461.1

    Aortic valve stenosis 421.3

    10.2

    31.1

    22.0

    00.0

    481.2

    Atrial septal defect 1,56449.3

    28359.6

    15253.6

    4241.0

    374.1

    2,07249.9

    Atrioventricular septal defect(Endocardial cushion defect)

    1043.3

    194.0

    82.8

    22.0

    00.0

    1363.3

    Biliary atresia 180.6

    51.1

    31.1

    00.0

    00.0

    260.6

    Bladder exstrophy 60.2

    10.2

    10.4

    00.0

    00.0

    80.2

    Choanal atresia 300.9

    30.6

    31.1

    00.0

    00.0

    370.9

    Cleft lip alone 882.8

    40.8

    62.1

    22.0

    00.0

    1012.4

    Cleft lip with cleft palate 2096.6

    142.9

    176.0

    54.9

    00.0

    2536.1

    Cleft palate alone 1906.0

    234.8

    62.1

    32.9

    00.0

    2245.4

    Cloacal exstrophy 531.7

    71.5

    31.1

    11.0

    00.0

    641.5

    Clubfoot 34510.9

    5411.4

    3713.0

    54.9

    00.0

    45310.9

    Coarctation of the aorta 1504.7

    102.1

    113.9

    22.0

    00.0

    1754.2

    Common truncus (truncus arteriosus) 100.3

    20.4

    00.0

    11.0

    00.0

    130.3

    Congenital cataract 120.4

    51.1

    31.1

    11.0

    00.0

    220.5

    Congenital posterior urethral valves 191.2

    31.2

    10.7

    00.0

    00.0

    241.1

    1

    Craniosynostosis 41012.9

    5010.5

    3010.6

    98.8

    124.7

    50912.3

    Deletion 22q11.2 70.2

    10.2

    20.7

    00.0

    00.0

    100.2

    Diaphragmatic hernia 852.7

    112.3

    103.5

    00.0

    00.0

    1102.6

    Double outlet right ventricle 481.5

    112.3

    51.8

    11.0

    00.0

    691.7

    Ebstein anomaly 120.4

    20.4

    10.4

    00.0

    00.0

    160.4

    Encephalocele 220.7

    10.2

    41.4

    00.0

    00.0

    280.7

    Esophageal atresia/tracheoesophagealfistula

    521.6

    40.8

    72.5

    00.0

    00.0

    631.5

    Gastroschisis 1023.2

    142.9

    113.9

    22.0

    00.0

    1333.2

    Holoprosencephaly 732.3

    71.5

    103.5

    11.0

    00.0

    962.3

    Hypoplastic left heart syndrome 702.2

    81.7

    72.5

    00.0

    00.0

    852.0

    Hypospadias 1,07966.2

    13957.6

    4027.7

    2750.6

    152.6

    1,30461.1

    1

    Interrupted aortic arch 190.6

    10.2

    31.1

    11.0

    00.0

    240.6

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S32

    Birth Defects Research 111: S1-S180 (2019)

  • IndianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 872.7

    142.9

    103.5

    22.0

    00.0

    1172.8

    Omphalocele 521.6

    102.1

    41.4

    43.9

    00.0

    711.7

    Pulmonary valve atresia and stenosis 2046.4

    296.1

    289.9

    32.9

    00.0

    2706.5

    Pulmonary valve atresia 280.9

    61.3

    72.5

    11.0

    00.0

    421.0

    Rectal and large intestinalatresia/stenosis

    1274.0

    183.8

    124.2

    32.9

    00.0

    1613.9

    Renal agenesis/hypoplasia 1354.3

    214.4

    93.2

    54.9

    00.0

    1744.2

    Single ventricle 130.4

    61.3

    31.1

    00.0

    00.0

    230.6

    Small intestinal atresia/stenosis 943.0

    204.2

    31.1

    65.9

    00.0

    1233.0

    Spina bifida without anencephalus 943.0

    51.1

    113.9

    22.0

    00.0

    1142.7

    Tetralogy of Fallot 882.8

    132.7

    51.8

    32.9

    124.7

    1132.7

    Total anomalous pulmonary venousconnection

    270.9

    30.6

    31.1

    00.0

    00.0

    330.8

    Transposition of the great arteries(TGA)

    682.1

    71.5

    72.5

    43.9

    00.0

    872.1

    Dextro-transposition of great arteries(d-TGA)

    591.9

    51.1

    62.1

    32.9

    00.0

    741.8

    Tricuspid valve atresia and stenosis 160.5

    61.3

    20.7

    32.9

    00.0

    280.7

    Trisomy 13 210.7

    40.8

    10.4

    00.0

    00.0

    270.7

    Trisomy 18 391.2

    71.5

    51.8

    11.0

    00.0

    521.3

    Trisomy 21 (Down syndrome) 42713.5

    5712.0

    5419.0

    109.8

    00.0

    55513.4

    Turner syndrome 312.0

    10.4

    00.0

    00.0

    00.0

    331.6

    2

    Ventricular septal defect 1,14436.1

    15933.5

    14852.2

    3534.2

    124.7

    1,51936.6

    Total live births 317,082 47,469 28,365 10,232 405 415,215

    Male live births 163,108 24,137 14,445 5,339 190 213,260

    Female live births 153,976 23,332 13,914 4,891 215 201,955

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S33

    Birth Defects Research 111: S1-S180 (2019)

  • IndianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IndianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 131

    3.620.4

    1333.2

    Trisomy 13 230.6

    40.8

    270.7

    Trisomy 18 290.8

    234.8

    521.3

    Trisomy 21 (Down syndrome) 3389.2

    21745.3

    55513.4

    Total live births 367,292 47,894 415,215

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.

    General comments*Data for totals include unknown and/or other.-Data for conditions are provisional.-Data for conditions include probable cases.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S34

    Birth Defects Research 111: S1-S180 (2019)

  • IowaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IowaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 231.4

    32.8

    53.0

    11.5

    00.0

    361.8

    Anophthalmia/microphthalmia 150.9

    43.8

    42.4

    23.0

    00.0

    251.3

    Anotia/microtia 342.1

    10.9

    74.2

    34.5

    00.0

    462.3

    Aortic valve stenosis 382.4

    00.0

    10.6

    11.5

    00.0

    412.1

    Atrial septal defect 46829.5

    4340.5

    4024.2

    1624.0

    111.7

    57729.4

    Atrioventricular septal defect(Endocardial cushion defect)

    764.8

    1110.4

    95.4

    34.5

    00.0

    1015.2

    Biliary atresia 40.3

    00.0

    00.0

    11.5

    00.0

    50.3

    Bladder exstrophy 70.4

    00.0

    00.0

    11.5

    00.0

    80.4

    Choanal atresia 130.8

    10.9

    10.6

    00.0

    00.0

    150.8

    1

    Cleft lip alone 563.5

    32.8

    137.9

    11.5

    111.7

    743.8

    Cleft lip with cleft palate 956.0

    43.8

    95.4

    34.5

    00.0

    1145.8

    Cleft palate alone 1066.7

    65.6

    84.8

    57.5

    00.0

    1276.5

    Cloacal exstrophy 20.1

    00.0

    00.0

    00.0

    00.0

    20.1

    Clubfoot 25816.3

    1615.1

    2816.9

    69.0

    335.0

    31716.2

    Coarctation of the aorta 1016.4

    00.0

    31.8

    11.5

    00.0

    1055.4

    Common truncus (truncus arteriosus) 110.7

    10.9

    31.8

    00.0

    00.0

    150.8

    Congenital cataract 664.2

    43.8

    53.0

    11.5

    111.7

    773.9

    Congenital posterior urethral valves 151.8

    11.9

    00.0

    12.9

    00.0

    171.7

    2

    Craniosynostosis 865.4

    32.8

    106.0

    46.0

    111.7

    1065.4

    Deletion 22q11.2 261.6

    32.8

    21.2

    11.5

    111.7

    331.7

    Diaphragmatic hernia 483.0

    10.9

    42.4

    34.5

    00.0

    593.0

    Double outlet right ventricle 221.4

    54.7

    74.2

    34.5

    00.0

    402.0

    Ebstein anomaly 150.9

    10.9

    31.8

    11.5

    00.0

    201.0

    Encephalocele 211.3

    00.0

    10.6

    00.0

    00.0

    231.2

    Esophageal atresia/tracheoesophagealfistula

    432.7

    21.9

    31.8

    23.0

    00.0

    502.5

    Gastroschisis 744.7

    65.6

    95.4

    00.0

    00.0

    904.6

    Holoprosencephaly 181.1

    32.8

    10.6

    00.0

    00.0

    241.2

    Hypoplastic left heart syndrome 352.2

    43.8

    42.4

    23.0

    00.0

    462.3

    Hypospadias 52965.0

    3056.3

    2833.7

    1543.0

    00.0

    60760.5

    2

    Interrupted aortic arch 90.6

    00.0

    00.0

    00.0

    00.0

    90.5

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S35

    Birth Defects Research 111: S1-S180 (2019)

  • IowaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 845.3

    32.8

    159.1

    34.5

    00.0

    1075.5

    3

    Omphalocele 372.3

    43.8

    42.4

    23.0

    111.7

    522.7

    Pulmonary valve atresia and stenosis 17511.0

    2018.8

    116.6

    710.5

    00.0

    21410.9

    Pulmonary valve atresia 90.6

    32.8

    00.0

    11.5

    00.0

    130.7

    Rectal and large intestinalatresia/stenosis

    513.2

    65.6

    84.8

    00.0

    00.0

    663.4

    Renal agenesis/hypoplasia 905.7

    54.7

    95.4

    11.5

    00.0

    1085.5

    Single ventricle 70.4

    00.0

    10.6

    00.0

    00.0

    80.4

    Small intestinal atresia/stenosis 583.7

    65.6

    31.8

    00.0

    00.0

    683.5

    Spina bifida without anencephalus 714.5

    32.8

    106.0

    00.0

    00.0

    854.3

    Tetralogy of Fallot 543.4

    32.8

    21.2

    46.0

    111.7

    643.3

    Total anomalous pulmonary venousconnection

    120.8

    10.9

    42.4

    23.0

    00.0

    191.0

    Transposition of the great arteries(TGA)

    432.7

    43.8

    31.8

    11.5

    00.0

    522.7

    Dextro-transposition of great arteries(d-TGA)

    382.4

    43.8

    31.8

    11.5

    00.0

    472.4

    Tricuspid valve atresia and stenosis 261.6

    43.8

    53.0

    11.5

    00.0

    361.8

    Tricuspid valve atresia 40.3

    21.9

    00.0

    11.5

    00.0

    70.4

    Trisomy 13 221.4

    54.7

    21.2

    00.0

    00.0

    311.6

    Trisomy 18 462.9

    21.9

    63.6

    57.5

    111.7

    653.3

    Trisomy 21 (Down syndrome) 21613.6

    1413.2

    2716.3

    57.5

    00.0

    27013.8

    Turner syndrome 314.0

    11.9

    56.1

    13.2

    00.0

    394.1

    4

    Ventricular septal defect 81351.2

    5047.1

    7444.7

    2639.0

    335.0

    97849.9

    Total live births 158,750 10,620 16,547 6,665 858 196,096 5

    Male live births 81,389 5,330 8,299 3,491 454 100,310

    Female live births 77,360 5,290 8,248 3,174 404 95,786

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S36

    Birth Defects Research 111: S1-S180 (2019)

  • IowaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)IowaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 88

    5.120.9

    904.6

    Trisomy 13 201.2

    114.8

    311.6

    Trisomy 18 362.1

    2912.5

    653.3

    Trisomy 21 (Down syndrome) 1619.3

    10947.1

    27013.8

    Total live births 172,954 23,135 196,096 5

    Notes1. Data for this condition exclude choanal stenosis.2. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.3. Data for this condition exclude other specified and unspecified limb reductions.4. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.5. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.-Data for conditions exclude probable/possible cases.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S37

    Birth Defects Research 111: S1-S180 (2019)

  • KansasBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)KansasBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 312.3

  • KansasBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Omphalocele 151.1

  • KansasBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)KansasBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 73

    4.4

  • KentuckyBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)KentuckyBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 411.8

    20.8

    21.4

    00.0

    00.0

    481.7

    Anophthalmia/microphthalmia 170.7

    31.3

    10.7

    00.0

    00.0

    230.8

    Anotia/microtia 110.5

    00.0

    53.6

    13.7

    00.0

    170.6

    Aortic valve stenosis 291.3

    10.4

    10.7

    00.0

    00.0

    351.3

    Atrial septal defect 6,130269.5

    1,104466.0

    362261.9

    140523.0

    9357.1

    8,199295.3

    Atrioventricular septal defect(Endocardial cushion defect)

    783.4

    145.9

    32.2

    13.7

    00.0

    1093.9

    Biliary atresia 70.3

    10.4

    00.0

    00.0

    00.0

    110.4

    Bladder exstrophy 60.3

    10.4

    00.0

    13.7

    00.0

    80.3

    Choanal atresia 241.1

    10.4

    00.0

    00.0

    00.0

    250.9

    Cleft lip alone 984.3

    41.7

    00.0

    414.9

    00.0

    1093.9

    Cleft lip with cleft palate 1597.0

    62.5

    64.3

    311.2

    00.0

    1806.5

    Cleft palate alone 1597.0

    93.8

    96.5

    13.7

    00.0

    1876.7

    Cloacal exstrophy 20.5

    00.0

    00.0

    00.0

    00.0

    20.4

    Clubfoot 42418.6

    3514.8

    2719.5

    933.6

    4158.7

    51618.6

    Coarctation of the aorta 1556.8

    145.9

    85.8

    13.7

    00.0

    1886.8

    Common truncus (truncus arteriosus) 200.9

    20.8

    10.7

    00.0

    00.0

    260.9

    Congenital cataract 261.1

    52.1

    00.0

    00.0

    00.0

    331.2

    Congenital posterior urethral valves 161.4

    10.8

    11.4

    17.3

    00.0

    191.3

    1

    Deletion 22q11.2 70.3

    00.0

    00.0

    00.0

    00.0

    70.3

    Diaphragmatic hernia 612.7

    73.0

    64.3

    27.5

    00.0

    812.9

    Double outlet right ventricle 512.2

    83.4

    00.0

    13.7

    00.0

    662.4

    Ebstein anomaly 180.8

    20.8

    10.7

    00.0

    00.0

    220.8

    Encephalocele 251.1

    31.3

    21.4

    00.0

    00.0

    341.2

    Esophageal atresia/tracheoesophagealfistula

    683.0

    41.7

    10.7

    00.0

    00.0

    752.7

    Gastroschisis 1145.0

    93.8

    75.1

    311.2

    00.0

    1385.0

    Holoprosencephaly 813.6

    83.4

    53.6

    13.7

    279.4

    1023.7

    Hypoplastic left heart syndrome 552.4

    41.7

    32.2

    00.0

    00.0

    702.5

    Hypospadias 1,00385.7

    9781.2

    3346.7

    1287.9

    00.0

    1,19583.8

    1

    Interrupted aortic arch 200.9

    20.8

    00.0

    00.0

    00.0

    271.0

    Limb deficiencies (reduction defects) 984.3

    83.4

    32.2

    27.5

    00.0

    1164.2

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S41

    Birth Defects Research 111: S1-S180 (2019)

  • KentuckyBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Omphalocele 441.9

    31.3

    00.0

    00.0

    00.0

    491.8

    Pulmonary valve atresia and stenosis 1406.2

    208.4

    85.8

    00.0

    00.0

    1776.4

    Pulmonary valve atresia 231.0

    31.3

    00.0

    00.0

    00.0

    281.0

    Rectal and large intestinalatresia/stenosis

    1185.2

    114.6

    107.2

    311.2

    00.0

    1495.4

    Renal agenesis/hypoplasia 1114.9

    93.8

    96.5

    311.2

    139.7

    1425.1

    Single ventricle 80.4

    20.8

    00.0

    00.0

    00.0

    120.4

    Small intestinal atresia/stenosis 823.6

    114.6

    64.3

    518.7

    00.0

    1154.1

    Spina bifida without anencephalus 602.6

    20.8

    64.3

    27.5

    00.0

    782.8

    Tetralogy of Fallot 914.0

    114.6

    32.2

    13.7

    00.0

    1164.2

    Total anomalous pulmonary venousconnection

    200.9

    31.3

    32.2

    00.0

    00.0

    311.1

    Transposition of the great arteries(TGA)

    652.9

    52.1

    10.7

    00.0

    00.0

    752.7

    Dextro-transposition of great arteries(d-TGA)

    602.6

    41.7

    10.7

    00.0

    00.0

    682.4

    Tricuspid valve atresia and stenosis 231.0

    20.8

    10.7

    00.0

    00.0

    271.0

    2

    Trisomy 13 271.2

    10.4

    10.7

    13.7

    00.0

    301.1

    Trisomy 18 492.2

    135.5

    53.6

    13.7

    00.0

    712.6

    Trisomy 21 (Down syndrome) 29913.1

    2912.2

    3122.4

    829.9

    00.0

    40614.6

    Turner syndrome 393.5

    21.7

    34.4

    00.0

    00.0

    473.5

    3

    Ventricular septal defect 1,30157.2

    13858.3

    8863.7

    2385.9

    279.4

    1,64659.3

    4

    Total live births 227,424 23,689 13,820 2,677 252 277,642 5

    Male live births 117,059 11,953 7,060 1,365 120 142,601

    Female live births 110,349 11,735 6,759 1,312 132 135,023

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S42

    Birth Defects Research 111: S1-S180 (2019)

  • KentuckyBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)KentuckyBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 135

    5.610.3

    1385.0

    Trisomy 13 251.0

    51.7

    301.1

    Trisomy 18 371.5

    3411.7

    712.6

    Trisomy 21 (Down syndrome) 24310.0

    13947.7

    40614.6

    Total live births 241,847 29,118 277,642 5

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include cases with stenosis and hypoplasia.3. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.4. Data for this condition exclude inlet ventricular septal defect and common atrioventricular canal type ventricular sepatal defect.5. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S43

    Birth Defects Research 111: S1-S180 (2019)

  • LouisianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)LouisianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 161.2

    111.2

  • LouisianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Omphalocele 231.8

    283.0

    00.0

    00.0

  • LouisianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)LouisianaBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 83

    3.7

  • MaineBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)MaineBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 132.2

    14.6

    00.0

    00.0

    00.0

    142.2

    1

    Anophthalmia/microphthalmia 20.4

    00.0

    00.0

    00.0

    00.0

    20.4

    2

    Anotia/microtia 122.1

    00.0

    00.0

    00.0

    00.0

    132.0

    Aortic valve stenosis 40.9

    00.0

    00.0

    00.0

    00.0

    40.8

    2

    Atrial septal defect 12426.6

    633.5

    669.7

    111.4

    236.9

    14428.4

    2

    Atrioventricular septal defect(Endocardial cushion defect)

    132.8

    15.6

    00.0

    00.0

    118.5

    163.2

    2

    Biliary atresia 00.0

    00.0

    00.0

    00.0

    00.0

    00.0

    2

    Bladder exstrophy 20.4

    00.0

    00.0

    00.0

    00.0

    20.4

    2

    Choanal atresia 71.2

    00.0

    00.0

    00.0

    00.0

    71.1

    Cleft lip alone 203.4

    00.0

    00.0

    00.0

    00.0

    213.3

    Cleft lip with cleft palate 376.3

    00.0

    00.0

    00.0

    114.9

    396.1

    Cleft palate alone 356.0

    14.6

    218.7

    19.0

    114.9

    416.4

    Coarctation of the aorta 284.8

    14.6

    00.0

    00.0

    00.0

    304.7

    Common truncus (truncus arteriosus) 00.0

    00.0

    00.0

    00.0

    00.0

    00.0

    Congenital cataract 20.4

    15.6

    00.0

    00.0

    00.0

    30.6

    2

    Diaphragmatic hernia 20.4

    00.0

    00.0

    00.0

    00.0

    20.4

    2

    Ebstein anomaly 10.2

    00.0

    00.0

    00.0

    00.0

    10.2

    2

    Encephalocele 71.2

    00.0

    00.0

    19.0

    00.0

    81.3

    Esophageal atresia/tracheoesophagealfistula

    132.8

    00.0

    00.0

    00.0

    00.0

    142.8

    2

    Gastroschisis 233.9

    00.0

    218.7

    00.0

    114.9

    274.2

    Hypoplastic left heart syndrome 172.9

    14.6

    00.0

    00.0

    00.0

    203.1

    Hypospadias 19765.5

    652.9

    235.1

    234.1

    128.3

    21966.8

    3

    Limb deficiencies (reduction defects) 193.3

    00.0

    00.0

    00.0

    00.0

    193.0

    Omphalocele 81.4

    00.0

    00.0

    00.0

    00.0

    81.3

    Pulmonary valve atresia and stenosis 356.0

    313.7

    00.0

    19.0

    00.0

    406.3

    Pulmonary valve atresia 71.2

    29.1

    00.0

    00.0

    00.0

    91.4

    Rectal and large intestinalatresia/stenosis

    224.7

    15.6

    00.0

    111.4

    00.0

    254.9

    2

    Renal agenesis/hypoplasia 316.6

    15.6

    111.6

    00.0

    00.0

    336.5

    2

    Spina bifida without anencephalus 162.7

    00.0

    00.0

    00.0

    00.0

    162.5

    Tetralogy of Fallot 325.5

    00.0

    19.4

    00.0

    00.0

    345.3

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S47

    Birth Defects Research 111: S1-S180 (2019)

  • MaineBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Transposition of the great arteries(TGA)

    152.6

    14.6

    19.4

    19.0

    00.0

    182.8

    Tricuspid valve atresia and stenosis 20.3

    14.6

    00.0

    00.0

    00.0

    30.5

    Tricuspid valve atresia 20.4

    00.0

    00.0

    00.0

    00.0

    20.4

    Trisomy 13 20.4

    00.0

    00.0

    00.0

    00.0

    20.4

    2

    Trisomy 18 71.5

    00.0

    00.0

    00.0

    00.0

    71.4

    2

    Trisomy 21 (Down syndrome) 6010.3

    522.9

    00.0

    218.0

    229.9

    7311.5

    Ventricular septal defect 9119.5

    422.4

    446.5

    00.0

    00.0

    10320.3

    2

    Total live births 58,448 2,188 1,069 1,113 669 63,584

    Male live births 30,076 1,134 569 586 353 32,768

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S48

    Birth Defects Research 111: S1-S180 (2019)

  • MaineBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)MaineBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 27

    5.000.0

    274.2

    Trisomy 13 20.5

    00.0

    20.4

    2

    Trisomy 18 40.9

    34.0

    71.4

    2

    Trisomy 21 (Down syndrome) 417.5

    2931.5

    7311.5

    Total live births 54,392 9,192 63,584

    Notes1. Data for this condition include probable cases.2. Data for this condition begin in 2013.3. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S49

    Birth Defects Research 111: S1-S180 (2019)

  • MarylandBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)MarylandBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 120.7

    60.5

    71.3

    00.0

    00.0

    361.0

    Anophthalmia/microphthalmia 10.1

    40.4

    10.2

    00.0

    00.0

    120.4

    Anotia/microtia 70.4

    00.0

    20.4

    00.0

    00.0

    130.4

    Aortic valve stenosis 20.1

    00.0

    00.0

    00.0

    00.0

    50.1

    Atrial septal defect 301.8

    332.8

    81.4

    10.4

    00.0

    1103.0

    Atrioventricular septal defect(Endocardial cushion defect)

    90.6

    60.5

    00.0

    00.0

    00.0

    310.8

    Biliary atresia 10.1

    00.0

    00.0

    00.0

    00.0

    10.0

    Bladder exstrophy 30.2

    10.1

    00.0

    00.0

    00.0

    70.2

    Choanal atresia 80.6

    40.4

    00.0

    10.5

    00.0

    150.5

    Cleft lip alone 281.7

    80.7

    81.4

    10.4

    00.0

    691.9

    Cleft lip with cleft palate 493.8

    151.6

    112.4

    20.9

    00.0

    1073.7

    Cleft palate alone 482.9

    242.0

    132.4

    41.5

    00.0

    1283.5

    Cloacal exstrophy 40.3

    50.5

    10.2

    00.0

    00.0

    120.4

    Clubfoot 311.9

    312.6

    162.9

    31.1

    00.0

    1283.5

    Coarctation of the aorta 161.2

    91.0

    10.2

    52.3

    00.0

    481.6

    Common truncus (truncus arteriosus) 30.2

    10.1

    00.0

    10.4

    00.0

    90.2

    Congenital cataract 10.1

    30.3

    10.2

    00.0

    00.0

    80.3

    Congenital posterior urethral valves 20.2

    10.2

    00.0

    00.0

    00.0

    50.3

    1

    Craniosynostosis 00.0

    00.0

    00.0

    00.0

    00.0

    40.1

    Deletion 22q11.2 20.2

    20.2

    00.0

    00.0

    00.0

    40.1

    Diaphragmatic hernia 171.0

    141.2

    10.2

    20.7

    00.0

    561.5

    Double outlet right ventricle 120.7

    151.3

    30.5

    31.1

    00.0

    491.3

    Ebstein anomaly 20.2

    20.2

    10.2

    00.0

    00.0

    70.2

    Encephalocele 40.2

    50.4

    10.2

    10.4

    00.0

    150.4

    Esophageal atresia/tracheoesophagealfistula

    261.6

    131.1

    20.4

    20.7

    00.0

    591.6

    Gastroschisis 291.8

    171.4

    20.4

    10.4

    00.0

    671.8

    Holoprosencephaly 60.4

    90.8

    50.9

    10.4

    00.0

    270.7

    Hypoplastic left heart syndrome 80.6

    80.8

    00.0

    10.5

    00.0

    351.2

    Hypospadias 24729.6

    15826.3

    7125.2

    2518.1

    00.0

    73639.5

    1

    Interrupted aortic arch 60.5

    50.5

    00.0

    10.5

    00.0

    220.8

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S50

    Birth Defects Research 111: S1-S180 (2019)

  • MarylandBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Limb deficiencies (reduction defects) 251.5

    292.5

    101.8

    20.7

    114.5

    892.4

    Omphalocele 70.4

    100.8

    00.0

    00.0

    114.5

    310.8

    Pulmonary valve atresia and stenosis 70.5

    91.0

    10.2

    20.9

    00.0

    341.2

    Pulmonary valve atresia 40.3

    40.4

    00.0

    10.5

    00.0

    130.4

    Rectal and large intestinalatresia/stenosis

    181.1

    161.4

    61.1

    31.1

    00.0

    531.5

    Renal agenesis/hypoplasia 110.7

    121.0

    71.3

    41.5

    00.0

    531.5

    Single ventricle 20.1

    30.3

    00.0

    10.4

    00.0

    70.2

    Small intestinal atresia/stenosis 80.5

    151.3

    10.2

    00.0

    00.0

    371.0

    Spina bifida without anencephalus 281.7

    161.4

    142.5

    20.7

    00.0

    742.0

    Tetralogy of Fallot 402.5

    141.2

    20.4

    51.9

    114.5

    842.3

    Total anomalous pulmonary venousconnection

    20.1

    00.0

    10.2

    00.0

    00.0

    70.2

    Transposition of the great arteries(TGA)

    60.5

    20.2

    00.0

    00.0

    00.0

    140.5

    Dextro-transposition of great arteries(d-TGA)

    50.3

    20.2

    00.0

    00.0

    00.0

    120.3

    Tricuspid valve atresia and stenosis 10.1

    40.3

    10.2

    10.4

    00.0

    130.4

    Tricuspid valve atresia 10.1

    40.3

    10.2

    10.4

    00.0

    130.4

    Trisomy 13 20.1

    60.5

    40.7

    00.0

    00.0

    290.8

    Trisomy 18 90.6

    161.4

    91.6

    00.0

    00.0

    681.9

    Trisomy 21 (Down syndrome) 976.0

    826.9

    5510.0

    124.5

    00.0

    3599.8

    Turner syndrome 40.5

    61.0

    10.4

    00.0

    00.0

    150.8

    2

    Ventricular septal defect 593.6

    726.1

    101.8

    62.2

    00.0

    2226.1

    Total live births 162,865 118,086 55,263 26,869 690 364,762 3

    Male live births 83,532 60,087 28,132 13,806 338 186,420

    Female live births 79,331 57,997 27,130 13,063 352 178,337

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S51

    Birth Defects Research 111: S1-S180 (2019)

  • MarylandBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)MarylandBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Age (Years)

    Defect Less than 35 35+ Total* NotesGastroschisis 39

    1.340.6

    671.8

    Trisomy 13 100.3

    101.4

    290.8

    Trisomy 18 270.9

    283.9

    681.9

    Trisomy 21 (Down syndrome) 1515.2

    14920.7

    3599.8

    Total live births 292,685 72,017 364,762 3

    Notes1. Data for this condition include male and unknown gender cases only. Prevalence is calculated per 10,000 male live births.2. Data for this condition include female and unknown gender cases only. Prevalance is calculated per 10,000 female live births.3. Data for total live births include unknown gender.

    General comments*Data for totals include unknown and/or other.

    STATE BIRTH DEFECTS SURVEILLANCE PROGRAM DATA S52

    Birth Defects Research 111: S1-S180 (2019)

  • MassachusettsBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)MassachusettsBirth Defects Counts and Prevalence 2012 - 2016 (Prevalence per 10,000 Live Births)

    Maternal Race/Ethnicity

    DefectWhite,Non-Hispanic

    Black,Non-Hispanic Hispanic

    Asian or PacificIslander,Non-Hispanic

    AmericanIndian orAlaska Native,Non-Hispanic Total* Notes

    Anencephalus 452.1

    72.0

    142.2

    61.9

    00.0

    852.4

    Anophthalmia/microphthalmia 251.1

    61.7

    111.7

    20.6

    00.0

    461.3

    Anotia/microtia 532.4

    82.3

    253.9

    61.9

    00.0

    952.6

    Aortic valve stenosis 401.8

    30.9

    40.6

    30.9

    00.0

    501.4

    Atrial septal defect 57426.2

    10530.0

    17126.7

    7422.9

    18.1

    94726.4

    Atrioventricular septal defect(Endocardial cushion defect)

    1135.1

    3810.8

    487.5

    113.4

    00.0

    2196.1

    Biliary atresia 80.4

    10.3

    40.6

    61.9

    00.0

    190.5

    Bladder exstrophy 80.4

    10.3

    20.3

    00.0

    00.0

    110.3

    Choanal atresia 190.9

    20.6

    40.6

    10.3

    00.0

    260.7

    Cleft lip alone 803.6

    92.6